Specific code 2014 ICD-9-CM Diagnosis Code 333.4
Huntington's chorea
  • Billable Code
  • ICD-9-CM 333.4 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 333.4 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Chorea, chronic progressive non hereditary
  • Chorea, progressive
  • Chorea, progressive non hereditary, chronic
  • Chronic progressive non-hereditary chorea (disorder)
  • Dementia due to Huntington chorea
  • Dementia due to Huntington chorea with altered behavior
  • Dementia due to Huntingtons chorea w behavior changes
  • Dementia due to Huntingtons disease
  • Dementia from huntingtons chorea
  • Huntingtons chorea
  • Progressive chorea
Clinical Information
  • A familial disorder inherited as an autosomal dominant trait and characterized by the onset of progressive chorea and dementia in the fourth or fifth decade of life. Common initial manifestations include paranoia; poor impulse control; depression; hallucinations; and delusions. Eventually intellectual impairment; loss of fine motor control; athetosis; and diffuse chorea involving axial and limb musculature develops, leading to a vegetative state within 10-15 years of disease onset. The juvenile variant has a more fulminant course including seizures; ataxia; dementia; and chorea. (from Adams et al., Principles of Neurology, 6th ed, pp1060-4)
  • A progressive hereditary neurodegenerative disorder inherited in an autosomal dominant fashion. Symptoms may appear at any age and include uncontrolled movements, clumsiness, balance problems, difficulty walking, talking, or swallowing. The disease has a progressive course with a decline in mental abilities, and the development of psychiatric problems.
  • Chronic progressive chorea and mental deterioration terminating in dementia; the age of onset usually is in the fourth decade of life.
  • Huntington's disease (hd) is an inherited disease that causes certain nerve cells in the brain to waste away. People are born with the defective gene, but symptoms usually don't appear until middle age. Early symptoms of hd may include uncontrolled movements, clumsiness or balance problems. Later, hd can take away the ability to walk, talk or swallow. Some people stop recognizing family members. Others are aware of their environment and are able to express emotions.if one of your parents has huntington's disease, you have a 50-50 chance of getting it. A blood test can tell if you have the hd gene and will develop the disease. Genetic counseling can help you weigh the risks and benefits of taking the test.there is no cure. Medicines can help manage some of the symptoms, but cannot slow down or stop the disease.
Convert to ICD-10-CM: 333.4 converts directly to:
  • 2014 ICD-10-CM G10 Huntington's disease
ICD-9-CM Volume 2 Index entries containing back-references to 333.4:
  • Chorea (gravis) (minor) (spasmodic) 333.5
    • chronic 333.4
    • hereditary 333.4
    • Huntington's 333.4
    • progressive 333.4
      • chronic 333.4
      • hereditary 333.4
  • Disease, diseased - see also Syndrome
    • Huntington's 333.4
  • Huntington's
    • chorea 333.4
    • disease 333.4
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 333.4 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.