- Hobo, hoboism V60.0
 - Hodgkin's
 - Hodgson's disease (aneurysmal dilatation of aorta) 441.9
 - Hodi-potsy 111.0
 - Hoffa (-Kastert) disease or syndrome (liposynovitis prepatellaris) 272.8
 - Hoffmann's syndrome 244.9 [359.5]
 - Hoffmann-Bouveret syndrome (paroxysmal tachycardia) 427.2
 - Hole
 - Holla disease (see also Spherocytosis) 282.0
 - Holländer-Simons syndrome (progressive lipodystrophy) 272.6
 - Hollow foot (congenital) 754.71
 - Holmes' syndrome (visual disorientation) 368.16
 - Holoprosencephaly 742.2
 - Holthouse's hernia - see Hernia, inguinal
 - Homesickness 309.89
 - Homicidal ideation V62.85
 - Homocystinemia 270.4
 - Homocystinuria 270.4
 - Homologous serum jaundice (prophylactic) (therapeutic) - see Hepatitis, viral
 - Homosexuality - omit code
 - Homozygous Hb-S disease 282.61
 - Honeycomb lung 518.89