Specific code 2015 ICD-9-CM Diagnosis Code 756.55
Chondroectodermal dysplasia
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 756.55 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 756.55 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 756.55 converts directly to:
  • 2015/16 ICD-10-CM Q77.6 Chondroectodermal dysplasia
Clinical Information
  • A rare autosomal recessive syndrome caused by mutations in the evc gene. It is characterized by dwarfism, small chest, ectodermal dysplasia, and postaxial polydactyly. There is an increased frequency of congenital heart malformations
  • Chondrodysplasia of long bones affecting mainly the distal ends of extremities and resulting in short-limb dwarfism, hexadactyly of the fingers and less frequently the toes; ectodermal dysplasia with nail and hair abnormalities, and congenital heart defects. Associated abnormalities may include cryptorchidism, epispadias, talipes equinovalgus, and dandy-walker syndrome (absence of cerebellar vermis, hydrocephalus, and posterior fossa cyst continuous with the fourth ventricle). Some patients are retarded. The largest pedigree was observed in old order amish in lancaster county, pennsylvania and some cases were reported in australian aborigines
  • Dwarfism occurring in association with defective development of skin, hair, and teeth, polydactyly, and defect of the cardiac septum. (Dorland, 27th ed)
Applies To
  • Ellis-van Creveld syndrome
ICD-9-CM Volume 2 Index entries containing back-references to 756.55:
  • Chondroectodermal dysplasia 756.55
  • Disease, diseased - see also Syndrome
    • Ellis-van Creveld (chondroectodermal dysplasia) 756.55
  • Dysplasia - see also Anomaly
    • chondroectodermal 756.55
  • Ellis-van Creveld disease or syndrome
    • (chondroectodermal dysplasia) 756.55
  • Syndrome - see also Disease
    • chondroectodermal dysplasia 756.55
    • Ellis-van Creveld (chondroectodermal dysplasia) 756.55
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 756.55 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.