Specific code 2014 ICD-9-CM Diagnosis Code 759.6
Other hamartoses, not elsewhere classified
  • Billable Code
  • Short description: Hamartoses NEC.
  • ICD-9-CM 759.6 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 759.6 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Angiomatosis of meninges
  • Astrocytic hamartoma
  • Cerebellar hemangioblastomatosis
  • Congenital erector pili hamartoma
  • Congenital hamartoma
  • Congenital hamartoma of skin
  • Congenital hamartosis
  • Congenital leptomeningeal angiomatosis
  • Cowden syndrome
  • Dermal connective tissue hamartoma
  • Diffuse smooth muscle hamartoma
  • Eccrine angiomatous hamartoma
  • Epidermal nevus
  • Epidermolytic epidermal nevus
  • Fat-storing hamartoma of dermal dendrocytes
  • Fibrolipomatous hamartoma of nerve
  • Hairy malformation of palms and soles
  • Hamartoma
  • Hamartoma of apocrine sweat gland apparatus
  • Hamartoma of eccrine sweat gland apparatus
  • Hamartoma of hypothalamus
  • Hamartoma of integument
  • Hamartoma of muscle
  • Hamartoma of pilosebaceous apparatus
  • Hamartoma of pituitary and hypothalamus
  • Hamartoma of retina
  • Hamartoma of skin
  • Hamartoma of skin appendage
  • Hereditary neurocutaneous angiomata
  • Lhermitte-Duclos disease
  • Lipomatous hamartoma
  • Moniliform hamartoma
  • Neoplasm and/or hamartoma
  • Neurocutaneous melanosis sequence
  • Parkes Weber syndrome
  • Peutz-Jeghers polyps of small bowel
  • Peutz-Jeghers syndrome
  • Retinal hamartoma
  • Riley-Smith syndrome
  • Spinal hamartoma
  • Splenic hamartoma
  • Sturge-Weber syndrome
  • Von Hippel-Lindau syndrome
Clinical Information
  • A group of neurocutaneous disorders manifested by facial and leptomeningeal angiomas, ipsilateral gyriform calcifications of the cerebral cortex, seizures, development delay, hemiplegia, emotional and behavioral problems, and glaucoma and other ocular disorders. Nevus flammeus on the side of the face ipsilateral to angiomatosis sometimes extends to neck, chest, and back. Angiomatosis may occasionally involve the choroid plexus, thyroid, pituitary gland, lungs, gastrointestinal organs, pancreas, ovaries, and thymus. Correlation between the distribution of the nevus and the course of the trigeminal nerve is responsible for naming the syndrome "trigemino-encephalo-angiomatosis," but later findings found the relationship to be fortuitous. The syndrome frequently occurs in incomplete forms, presenting different combinations of symptoms.
  • A rare inherited disorder in which blood vessels grow abnormally in the eyes, brain, spinal cord, adrenal glands, or other parts of the body. People with von hippel-lindau syndrome have a higher risk of developing some types of cancer.
  • An inherited condition characterized by generalized hamartomatous multiple polyposis of the intestinal tract. Transmitted in an autosomal dominant fashion, peutz-jeghers syndrome consistently involves the jejunum and is associated with melanin spots of the lips, buccal mucosa, and fingers. This syndrome is associated with abnormalities of chromosome 19. Also known as jeghers-peutz syndrome and peutz's syndrome.
  • An inherited familial cancer syndrome which is characterized by development of capillary hemangioblastomas of the central nervous system and retina; clear cell renal carcinoma; pheochromocytoma; pancreatic tumors; and inner ear tumors. The syndrome is associated with germline mutations of the vhl tumor suppressor gene, located on chromosome 3p25-26. Symptoms of vhl syndrome may not be apparent until the third decade of life. Cns hemangioblastoma is the most common cause of death, followed by clear cell renal cell carcinoma.
  • Autosomal dominant disorder associated with cerebellar and retinal neoplasms; the most common manifestations are neurologic deficits associated with intracranial hemangioblastomas which may hemorrhage, causing ataxia, intracranial hypertension, and other signs of neurologic dysfunction.
759.6 Excludes
Applies To
  • Syndrome:
    • Peutz-Jeghers
    • Sturge-Weber (-Dimitri)
    • von Hippel-Lindau
Convert to ICD-10-CM: 759.6 converts approximately to:
  • 2014 ICD-10-CM Q85.8 Other phakomatoses, not elsewhere classified
ICD-9-CM Volume 2 Index entries containing back-references to 759.6:
  • Amentia (see also Disability, intellectual) 319
    • nevoid 759.6
  • Angiomatosis 757.32
    • cutaneocerebral 759.6
    • encephalocutaneous 759.6
    • encephalofacial 759.6
    • encephalotrigeminal 759.6
    • meningo-oculofacial 759.6
    • neuro-oculocutaneous 759.6
    • retina (Hippel's disease) 759.6
    • retinocerebellosa 759.6
    • retinocerebral 759.6
  • Dimitri-Sturge-Weber disease (encephalocutaneous angiomatosis) 759.6
  • Disease, diseased - see also Syndrome
    • Dimitri-Sturge-Weber (encephalocutaneous angiomatosis) 759.6
    • Hippel's (retinocerebral angiomatosis) 759.6
    • Kalischer's 759.6
    • Kraft-Weber-Dimitri 759.6
    • Lagleyze-von Hippel (retinocerebral angiomatosis) 759.6
    • Lindau's (retinocerebral angiomatosis) 759.6
    • Lindau-von Hippel (angiomatosis retinocerebellosa) 759.6
    • Peutz-Jeghers 759.6
    • Sturge (-Weber) (-Dimitri) (encephalocutaneous angiomatosis) 759.6
    • von Hippel's (retinocerebral angiomatosis) 759.6
    • von Hippel-Lindau (angiomatosis retinocerebellosa) 759.6
  • Dysplasia - see also Anomaly
    • neuroectodermal 759.6
  • Hamartoblastoma 759.6
  • Hamartoma 759.6
    • epithelial (gingival), odontogenic, central, or peripheral (M9321/0) 213.1
  • Hamartosis, hamartoses NEC 759.6
  • Hemangioblastomatosis, cerebelloretinal 759.6
  • Hippel's disease (retinocerebral angiomatosis) 759.6
  • Jahnke's syndrome (encephalocutaneous angiomatosis) 759.6
  • Kalischer's syndrome (encephalocutaneous angiomatosis) 759.6
  • Krabbe's
    • syndrome
      • congenital muscle hypoplasia 756.89
      • cutaneocerebral angioma 759.6
  • Kraft-Weber-Dimitri disease 759.6
  • Lagleyze-von Hippel disease (retinocerebral angiomatosis) 759.6
  • Lawford's syndrome (encephalocutaneous angiomatosis) 759.6
  • Lindau's disease (retinocerebral angiomatosis) 759.6
  • Lindau (-von Hippel) disease (angiomatosis retinocerebellosa) 759.6
  • Milles' syndrome (encephalocutaneous angiomatosis) 759.6
  • Neuroangiomatosis, encephalofacial 759.6
  • Parkes Weber and Dimitri syndrome (encephalocutaneous angiomatosis) 759.6
  • Peutz-Jeghers disease or syndrome 759.6
  • Schirmer's syndrome (encephalocutaneous angiomatosis) 759.6
  • Sturge (-Weber) (-Dimitri) disease or syndrome (encephalocutaneous angiomatosis) 759.6
  • Sturge-Kalischer-Weber syndrome (encephalocutaneous angiomatosis) 759.6
  • Syndrome - see also Disease
    • Cowden 759.6
    • Jahnke's (encephalocutaneous angiomatosis) 759.6
    • Kalischer's (encephalocutaneous angiomatosis) 759.6
    • Krabbe's
      • congenital muscle hypoplasia 756.89
      • cutaneocerebral angioma 759.6
    • Lawford's (encephalocutaneous angiomatosis) 759.6
    • Milles' (encephalocutaneous angiomatosis) 759.6
    • neurocutaneous 759.6
    • Parkes Weber and Dimitri (encephalocutaneous angiomatosis) 759.6
    • Peutz-Jeghers 759.6
    • Schirmer's (encephalocutaneous angiomatosis) 759.6
    • Sturge-Kalischer-Weber (encephalotrigeminal angiomatosis) 759.6
    • Sturge-Weber (-Dimitri) (encephalocutaneous angiomatosis) 759.6
    • von Hippel-Lindau (angiomatosis retinocerebellosa) 759.6
    • Weber-Dimitri (encephalocutaneous angiomatosis) 759.6
  • Trigeminoencephaloangiomatosis 759.6
  • von Hippel (-Lindau) disease or syndrome (retinocerebral angiomatosis) 759.6
  • Weber-Dimitri syndrome 759.6
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 759.6 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.