2013 ICD-9-CM Diagnosis Code 202.5
Letterer-siwe disease
- A multifocal, multisystem form of Langerhans-cell histiocytosis. There is involvement of multiple organ systems including the bones, skin, liver, spleen, and lymph nodes. Patients are usually infants presenting with fever, hepatosplenomegaly, lymphadenopathy, bone and skin lesions, and pancytopenia.
- There are 9 ICD-9-CM codes below 202.5 that define this diagnosis in greater detail. Do not use this code on a reimbursement claim.
202.5 Excludes 
)Applies To
ICD-9-CM Volume 2 Index entries containing back-references to 202.5:
Letterer-Siwe (acute histiocytosis X) (M9722/3) 
acute differentiated progressive (M9722/3) 
