Non-specific code 2014 ICD-9-CM Diagnosis Code 202.5
Letterer-siwe disease
  • Non-Billable Code
  • There are 9 ICD-9-CM codes below 202.5 that define this diagnosis in greater detail. Do not use this code on a reimbursement claim.
Clinical Information
  • A multifocal, multisystem form of langerhans-cell histiocytosis. There is involvement of multiple organ systems including the bones, skin, liver, spleen, and lymph nodes. Patients are usually infants presenting with fever, hepatosplenomegaly, lymphadenopathy, bone and skin lesions, and pancytopenia.
202.5 Excludes
  • adult pulmonary Langerhans cell histiocytosis (516.5)
  • Hand-Schüller-Christian disease (277.89)
  • histiocytosis (acute) (chronic) (277.89)
  • histiocytosis X (chronic) (277.89)
Applies To
  • Acute:
    • differentiated progressive histiocytosis
    • histiocytosis X (progressive)
    • infantile reticuloendotheliosis
    • reticulosis of infancy
ICD-9-CM Volume 2 Index entries containing back-references to 202.5:
  • Abt-Letterer-Siwe syndrome (acute histiocytosis X) (M9722/3) 202.5
  • Disease, diseased - see also Syndrome
    • Letterer-Siwe (acute histiocytosis X) (M9722/3) 202.5
  • Histiocytosis (acute) (chronic) (subacute) 277.89
    • acute differentiated progressive (M9722/3) 202.5
    • X (chronic) 277.89
      • acute (progressive) (M9722/3) 202.5
  • Letterer-Siwe disease (acute histiocytosis X) (M9722/3) 202.5
  • Reticuloendotheliosis
    • acute infantile (M9722/3) 202.5
    • nonlipid (M9722/3) 202.5
  • Reticulosis (skin)
    • acute of infancy (M9722/3) 202.5
  • Syndrome - see also Disease
    • Abt-Letterer-Siwe (acute histiocytosis X) (M9722/3) 202.5
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 202.5 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.