756.55 is a billable ICD-9-CM medical code that can be used to specify a diagnosis on a reimbursement claim.
Diagnosis Definition(s)
Chondrodysplasia of long bones affecting mainly the distal ends of extremities and resulting in short-limb dwarfism, hexadactyly of the fingers and less frequently the toes; ectodermal dysplasia with nail and hair abnormalities, and congenital heart defects. Associated abnormalities may include cryptorchidism, epispadias, talipes equinovalgus, and Dandy-Walker syndrome (absence of cerebellar vermis, hydrocephalus, and posterior fossa cyst continuous with the fourth ventricle). Some patients are retarded. The largest pedigree was observed in Old Order Amish in Lancaster County, Pennsylvania and some cases were reported in Australian Aborigines.
Also applicable to/known as
Ellis-van Creveld syndrome
ICD-9-CM Volume 2 Index Entries That Refer To 756.55
2010 ICD-9-CM Diagnosis Code 756.55
756.55