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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Musculoskeletal System And Connective Tissue 710-739 > Arthropathies And Related Disorders 710-719 > Diffuse Diseases Of Connective Tissue 710.* >

2007 ICD-9-CM Diagnosis 710.3

Dermatomyositis

This code may be outdated. View the most recent version of ICD-9-CM 710.3

  • A subacute or chronic inflammatory disease of muscle and skin, marked by proximal muscle weakness and a characteristic skin rash. The illness occurs with approximately equal frequency in children and adults. The skin lesions usually take the form of a purplish rash (or less often an exfoliative dermatitis) involving the nose, cheeks, forehead, upper trunk, and arms. The disease is associated with a complement mediated intramuscular microangiopathy, leading to loss of capillaries, muscle ischemia, muscle-fiber necrosis, and perifascicular atrophy. The childhood form of this disease tends to evolve into a systemic vasculitis. Dermatomyositis may occur in association with malignant neoplasms. (From Adams et al., Principles of Neurology, 6th ed, pp1405-6)
  • 710.3 is a specific code that can be used to specify a diagnosis
  • 710.3 contains 12 index entries
  • View the ICD-9-CM Volume 1 710.* hierarchy

710.3 also known as:

  • Poikilodermatomyositis
  • Polymyositis with skin involvement

Index entries containing 710.3:

Dermatomucomyositis 710.3
Dermatomyositis (acute) (chronic) 710.3
Petges-Cléjat or Petges-Clégat syndrome (poikilodermatomyositis) 710.3
Poikilodermatomyositis 710.3
Polymyositis (acute) (chronic) (hemorrhagic) 710.4
  • with involvement of
    • skin 710.3
  • Wagner's (dermatomyositis) 710.3
Pseudotrichinosis 710.3
Syndrome - see also Disease
  • Petges-Cléjat (poikilodermatomyositis) 710.3
  • Unverricht-Wagner (dermatomyositis) 710.3
  • Wagner (-Unverricht) (dermatomyositis) 710.3
Unverricht-Wagner syndrome (dermatomyositis) 710.3
Wagner (-Unverricht) syndrome (dermatomyositis) 710.3