2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Disorders Of The Peripheral Nervous System 350-359 > Hereditary And Idiopathic Peripheral Neuropathy 356.* >
 2007 ICD-9-CM Diagnosis 356.3
Refsum's disease On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date.
The 2009 version of ICD-9-CM 356.3 can be accessed here. - An autosomal recessive familial disorder that usually presents in childhood with POLYNEUROPATHY, sensorineural DEAFNESS; ICHTHYOSIS; ATAXIA; RETINITIS PIGMENTOSA; and cardiomyopathy. CEREBROSPINAL FLUID PROTEINS and serum PHYTANIC ACID are generally elevated. This condition is associated with the impaired metabolism of phytanic acid in PEROXISOMES. (From Joynt, Clinical Neurology, 1991, Ch37, p58-9; Rev Med Interne 1996;17(5):391-8)
- 356.3 is a specific code that can be used to specify a diagnosis
- 356.3 contains 6 index entries
- View the ICD-9-CM Volume 1 356.* hierarchy
356.3 also known as:- Heredopathia atactica polyneuritiformis
Index entries containing 356.3:- Disease, diseased - see also Syndrome
- Refsum's (heredopathia atactica polyneuritiformis)
 356.3
Heredopathia atactica polyneuritiformis 356.3
Neuropathy, neuropathic (see also Disorder, nerve) 355.9- hypertrophic
- Refsum 356.3
Polyneuritis, polyneuritic (see also Polyneuropathy) 356.9- hereditary ataxic 356.3
Refsum's disease or syndrome (heredopathia atactica polyneuritiformis) 356.3
Syndrome - see also Disease- Refsum's (heredopathia atactica polyneuritiformis) 356.3
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