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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Other Metabolic Disorders And Immunity Disorders 270-279 > Disorders Involving The Immune Mechanism 279.* >

2007 ICD-9-CM Diagnosis 279.04

Congenital hypogammaglobulinemia

This code may be outdated. View the most recent version of ICD-9-CM 279.04

  • X-linked agammaglobulinemia. An immunodeficiency state characterized (usually) by profoundly low concentrations of serum immunoglobulins of all classes, although occasionally significant amounts of one or more isotypes can be found. The fundamental defect in XLA affects early lineage B cells.
  • 279.04 is a specific code that can be used to specify a diagnosis
  • 279.04 contains 7 index entries
  • View the ICD-9-CM Volume 1 279.* hierarchy

279.04 also known as:

  • Agammaglobulinemia:
    • Bruton's type
    • X-linked

Index entries containing 279.04:

Agammaglobulinemia 279.00
  • Bruton's X-linked 279.04
  • infantile sex-linked (Bruton's) (congenital) 279.04
Antibody deficiency syndrome
  • congenital 279.04
Bruton's X-linked agammaglobulinemia 279.04
Deficiency, deficient
  • humoral 279.00
    • congenital hypogammaglobulinemia 279.04
Disease, diseased - see also Syndrome
  • Bruton's (X-linked agammaglobulinemia) 279.04
Syndrome - see also Disease
  • antibody deficiency 279.00
    • congenital 279.04