Specific code 2014 ICD-9-CM Diagnosis Code 279.04
Congenital hypogammaglobulinemia
  • Billable Code
  • Short description: Cong hypogammaglobulinem.
  • ICD-9-CM 279.04 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 279.04 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Agammaglobulinemia, X linked
  • Congenital agammaglobulinemia
  • Hypogammaglobulinemia, congenital
  • X linked agammaglobulinemia
  • X linked hypogammaglobulinemia
  • X-linked agammaglobulinemia
  • X-linked hypogammaglobulinemia
Clinical Information
  • X-linked agammaglobulinemia. An immunodeficiency state characterized (usually) by profoundly low concentrations of serum immunoglobulins of all classes, although occasionally significant amounts of one or more isotypes can be found. The fundamental defect in xla affects early lineage b cells.
Applies To
  • Agammaglobulinemia:
    • Bruton's type
    • X-linked
Convert to ICD-10-CM: 279.04 converts directly to:
  • 2014 ICD-10-CM D80.0 Hereditary hypogammaglobulinemia
ICD-9-CM Volume 2 Index entries containing back-references to 279.04:
  • Agammaglobulinemia 279.00
    • Bruton's X-linked 279.04
    • infantile sex-linked (Bruton's) (congenital) 279.04
  • Antibody
    • deficiency syndrome
      • agammaglobulinemic 279.00
      • congenital 279.04
      • hypogammaglobulinemic 279.00
  • Bruton's X-linked agammaglobulinemia 279.04
  • Deficiency, deficient
  • Disease, diseased - see also Syndrome
    • Bruton's (X-linked agammaglobulinemia) 279.04
  • Syndrome - see also Disease
    • antibody deficiency 279.00
      • agammaglobulinemic 279.00
      • congenital 279.04
      • hypogammaglobulinemic 279.00
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 279.04 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.