Home > 2015 ICD-9-CM Diagnosis Codes > Congenital Anomalies 740-759 > Congenital anomalies of the integument 757-
Specific code 2015 ICD-9-CM Diagnosis Code 757.33
Congenital pigmentary anomalies of skin
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 757.33 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 757.33 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 757.33 converts approximately to:
  • 2015/16 ICD-10-CM Q82.1 Xeroderma pigmentosum
    Or:
  • 2015/16 ICD-10-CM Q82.2 Mastocytosis
Approximate Synonyms
  • Anomaly of skin pigment, congenital
  • Congenital anomaly of skin pigment
  • Congenital pigmentary skin anomalies
  • Incontinentia pigmenti syndrome
  • Mongolian spot
  • Mongolian spot (blue/gray skin discoloration)
  • Urticaria pigmentosa
  • Xeroderma pigmentosum
Clinical Information
  • A genetic condition characterized by a sensitivity to all sources of ultraviolet radiation
  • An inherited skin disorder characterized by photosensitivity with severe sunburn in infancy, the development of numerous pigmented spots resembling freckles, larger atrophic lesions associated with telangiectasis, and multiple solar keratoses. Transmitted in an autosomal recessive manner, xeroderma pigmentosa involves a defect in nucleotide excision repair (ner), leading to deficient repair of dna damaged by uv radiation and chromosome breakage. Individuals with this disease develop multiple malignant cutaneous neoplasms at an early age and may suffer from severe ophthalmic and neurologic abnormalities
  • Most common form of mastocytosis, characterized by multiple persistant small reddish brown hyperpigmented pruritic macules and papules
  • Rare pigmentary atrophic autosomal recessive disease manifested as an extreme photosensitivity to ultraviolet light as the result of a deficiency in the enzyme that permits excisional repair of utraviolet damaged dna
  • The most frequent form of cutaneous mastocytosis. In children, the lesions tend to be papular, and are characterized by aggregates of elongated or spindle-shaped mast cells which fill the papillary dermis and extend into the reticular dermis. In adults, the lesions tend to have fewer mast cells compared to those in children. The lesions are located most commonly on the trunk, but they can be seen on the extremities, head and neck. (who, 2001)
757.33 Excludes
Applies To
  • Congenital poikiloderma
  • Urticaria pigmentosa
  • Xeroderma pigmentosum
ICD-9-CM Volume 2 Index entries containing back-references to 757.33:
  • Angioma (M9120/0) (see also Hemangioma, by site) 228.00
    • pigmentosum et atrophicum 757.33
  • Anomaly, anomalous (congenital) (unspecified type) 759.9
  • Asboe-Hansen's disease (incontinentia pigmenti) 757.33
  • Atrophoderma, atrophodermia 701.9
    • pigmentosum 757.33
  • Bloch-Siemens syndrome (incontinentia pigmenti) 757.33
  • Bloch-Stauffer dyshormonal dermatosis 757.33
  • Bloch-Sulzberger disease or syndrome (incontinentia pigmenti) (melanoblastosis) 757.33
  • Chloasma 709.09
  • Dermatosis 709.9
  • Disease, diseased - see also Syndrome
    • Asboe-Hansen's (incontinentia pigmenti) 757.33
    • Bloch-Sulzberger (incontinentia pigmenti) 757.33
    • xeroderma pigmentosum 757.33
    • mast cell 757.33
    • Nettleship's (urticaria pigmentosa) 757.33
    • Thomson's (congenital poikiloderma) 757.33
  • Incontinentia pigmenti 757.33
  • Kaposi's
    • xeroderma pigmentosum 757.33
  • Lioderma essentialis (cum melanosis et telangiectasia) 757.33
  • Mast cell
    • disease 757.33
  • Mastocytosis 757.33
    • malignant (M9741/3) 202.6
  • Melanoblastosis
    • Block-Sulzberger 757.33
    • cutis linearis sive systematisata 757.33
  • Melanocytosis, neurocutaneous 757.33
  • Melanosis 709.09
    • corii degenerativa 757.33
    • lenticularis progressiva 757.33
  • Mongolian, mongolianism, mongolism, mongoloid 758.0
    • spot 757.33
  • Naegeli's
    • syndrome (incontinentia pigmenti) 757.33
  • Nettleship's disease (urticaria pigmentosa) 757.33
  • Nevus (M8720/0) - see also Neoplasm, skin, benign
    • comedonicus 757.33
    • pigmented (M8720/0)
      • giant (M8761/1) - see also Neoplasm, skin, uncertain behavior
        • malignant melanoma in (M8761/3) - see Melanoma
      • systematicus 757.33
    • unius lateris 757.33
    • verrucous 757.33
  • Pigmentation (abnormal) 709.00
    • lids (congenital) 757.33
    • scrotum, congenital 757.33
  • Poikiloderma 709.09
    • congenital 757.33
  • Rothmund (-Thomson) syndrome 757.33
  • Spots, spotting
    • Mongolian (pigmented) 757.33
  • Syndrome - see also Disease
    • Block-Siemens (incontinentia pigmenti) 757.33
    • Bloch-Sulzberger (incontinentia pigmenti) 757.33
    • mastocytosis 757.33
    • Rothmund's (congenital poikiloderma) 757.33
    • telangiectasis-pigmentation-cataract 757.33
  • Thomson's disease (congenital poikiloderma) 757.33
  • Urticaria 708.9
    • pigmentosa 757.33
  • Xanthelasmoidea 757.33
  • Xeroderma (congenital) 757.39
    • pigmentosum 757.33
 757.32 ICD9Data.com 757.39 
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