Specific code 2015 ICD-9-CM Diagnosis Code 286.1
Congenital factor IX disorder
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 286.1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 286.1 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 286.1 converts directly to:
  • 2015/16 ICD-10-CM D67 Hereditary factor IX deficiency
Approximate Synonyms
  • Acquired factor IX deficiency disease
  • Acquired hemophilia b
  • Hemophilia B
  • Hemophilia B, acquired
  • Hereditary factor IX deficiency disease
Clinical Information
  • A deficiency of blood coagulation factor ix inherited as an x-linked disorder. (also known as christmas disease, after the first patient studied in detail, not the holy day.) historical and clinical features resemble those in classic hemophilia (hemophilia a), but patients present with fewer symptoms. Severity of bleeding is usually similar in members of a single family. Many patients are asymptomatic until the hemostatic system is stressed by surgery or trauma. Treatment is similar to that for hemophilia a. (from cecil textbook of medicine, 19th ed, p1008)
  • An x-linked inherited bleeding disorder caused by deficiency of the coagulation factor ix
  • Deficiency of blood coagulation factor ix inherited as an x-linked disorder; clinical features resemble those in hemophilia a, but patients present with fewer symptoms
Applies To
  • Christmas disease
  • Deficiency:
    • factor IX (functional)
    • plasma thromboplastin component [PTC]
  • Hemophilia B
ICD-9-CM Volume 2 Index entries containing back-references to 286.1:
  • Christmas disease 286.1
  • Deficiency, deficient
    • autoprothrombin
      • I (see also Defect, coagulation) 286.3
      • II 286.1
      • C (see also Defect, coagulation) 286.3
    • Christmas factor 286.1
    • factor (see also Defect, coagulation) 286.9
      • I (congenital) (fibrinogen) 286.3
        • antepartum or intrapartum 641.3
          • affecting fetus or newborn 762.1
        • newborn, transient 776.3
        • postpartum 666.3
      • II (congenital) (prothrombin) 286.3
      • V (congenital) (labile) 286.3
      • VII (congenital) (stable) 286.3
      • VIII (congenital) (functional) 286.0
      • IX (Christmas) (congenital) (functional) 286.1
      • X (congenital) (Stuart-Prower) 286.3
      • XI (congenital) (plasma thromboplastin antecedent) 286.2
      • XII (congenital) (Hageman) 286.3
      • XIII (congenital) (fibrin stabilizing) 286.3
      • hageman 286.3
      • multiple (congenital) 286.9
    • plasma
      • cell 279.00
      • protein (paraproteinemia) (pyroglobulinemia) 273.8
      • thromboplastin
        • antecedent (PTA) 286.2
        • component (PTC) 286.1
    • PTC 286.1
  • Disease, diseased - see also Syndrome
    • Christmas 286.1
  • Disorder - see also Disease
    • coagulation (factor) (see also Defect, coagulation) 286.9
      • factor VIII (congenital) (functional) 286.0
      • factor IX (congenital) (functional) 286.1
      • neonatal, transitory 776.3
    • factor, coagulation (see also Defect, coagulation) 286.9
      • VIII (congenital) (functional) 286.0
      • IX (congenital) (functional) 286.1
  • Hemophilia (familial) (hereditary) 286.0
    • B (Leyden) 286.1
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 286.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.