Specific code 2015 ICD-9-CM Diagnosis Code 277.00
Cystic fibrosis without mention of meconium ileus
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 277.00 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 277.00 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 277.00 converts directly to:
  • 2015/16 ICD-10-CM E84.9 Cystic fibrosis, unspecified
Approximate Synonyms
  • Cystic fibrosis
Clinical Information
  • A common hereditary disease in which exocrine (secretory) glands produce abnormally thick mucus. This mucus can cause problems in digestion, breathing, and body cooling
  • A congenital metabolic disorder affecting the exocrine glands, inherited as an autosomal trait. The secretions of exocrine glands are abnormal, resulting in excessively viscid mucus production which causes obstruction of passageways (including pancreatic and bile ducts, intestines, and bronchi). The sweat sodium and chloride content are increased. Symptoms usually appear in childhood and include meconium ileus, poor growth despite good appetite, malabsorption and foul bulky stools, chronic bronchitis with cough, recurrent pneumonia, bronchiectasis, emphysema, clubbing of the fingers, and salt depletion in hot weather
  • Most common potentially lethal autosomal recessive disease affecting caucasians; characterized by chronic pulmonary, intestinal, liver, pancreatic, and exocrine gland dysfunction; caused by mutations of the cftr chloride channel
Applies To
  • Cystic fibrosis NOS
ICD-9-CM Volume 2 Index entries containing back-references to 277.00:
  • Cirrhosis, cirrhotic 571.5
    • due to
      • bronzed diabetes 275.01
      • congestive hepatomegaly - see Cirrhosis, cardiac
      • cystic fibrosis 277.00
      • hemochromatosis (see also Hemochromatosis) 275.03
      • hepatolenticular degeneration 275.1
      • passive congestion (chronic) - see Cirrhosis, cardiac
      • Wilson's disease 275.1
  • Cystic - see also condition
    • fibrosis (pancreas) 277.00
  • Disease, diseased - see also Syndrome
  • Fibrocystic
  • Fibrosis, fibrotic
    • cystic (of pancreas) 277.00
  • Hyperviscidosis 277.00
  • Mucoviscidosis 277.00
    • with meconium obstruction 277.01
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.00 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.