- van Bogaert's leukoencephalitis (sclerosing) (subacute) 046.2
- van Bogaert-Nijssen (-Peiffer) disease 330.0
- van Buchem's syndrome (hyperostosis corticalis) 733.3
- van Creveld-von Gierke disease (glycogenosis I) 271.0
- van den Bergh's disease (enterogenous cyanosis) 289.7
- van der Hoeve's syndrome (brittle bones and blue sclera, deafness) 756.51
- van der Hoeve-Halbertsma-Waardenburg syndrome (ptosis-epicanthus) 270.2
- van der Hoeve-Waardenburg-Gualdi syndrome (ptosis-epicanthus) 270.2
- van Neck (-Odelberg) disease or syndrome (juvenile osteochondrosis) 732.1
- Vancomycin (glycopeptide)
- Vanillism 692.89
- Vanishing lung 492.0
- Vanishing twin 651.33
- Vapor asphyxia or suffocation NEC 987.9
- Vaquez's disease (M9950/1) 238.4
- Vaquez-Osler disease (polycythemia vera) (M9950/1) 238.4
- Variance, lethal ball, prosthetic heart valve 996.02
- Variants, thalassemic 282.49
- Variations in hair color 704.3
- Varicella 052.9
- Varices - see Varix
- Varicocele (scrotum) (thrombosed) 456.4