Specific code 2015 ICD-9-CM Diagnosis Code 516.4
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015
  • Female Only Dx

  • ICD-9-CM 516.4 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 516.4 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 516.4 converts directly to:
  • 2015/16 ICD-10-CM J84.81 Lymphangioleiomyomatosis
Approximate Synonyms
  • Lymphangiomyomatosis
  • Lymphangiomyomatosis, pulmonary
  • Pulmonary lymphangioleiomyomatosis
Clinical Information
  • A disease characterized by the progressive invasion of smooth muscle cells into the lymphatic vessels, and the blood vessels. The majority of the cases occur in the lungs of women of child-bearing age, eventually blocking the flow of air, blood, and lymph. The common symptom is shortness of breath (dyspnea)
  • A multifocal neoplasm with perivascular epithelioid cell differentiation affecting almost exclusively females of child-bearing age. It is characterized by the presence of smooth muscle and epithelioid cells and by the proliferation of lymphatic vessels. Sites of involvement include the lungs, mediastinum, and the retroperitoneum. It usually presents with chylous pleural effusion or ascites
  • Rare lung disorder of unknown etiology mostly in women of childbearing age; proliferation of atypical smooth muscle cells in lungs, airways, blood and lymph vessels causing obstruction; symptoms include dyspnea and pneumothorax
Applies To
  • Lymphangiomyomatosis
ICD-9-CM Coding Information
  • 516.4 is only applicable to female patients.
ICD-9-CM Volume 2 Index entries containing back-references to 516.4:
  • Lymphangioleiomyomatosis 516.4
  • Lymphangiomyomatosis 516.4
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 516.4 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.