Specific code 2015 ICD-9-CM Diagnosis Code 359.1
Hereditary progressive muscular dystrophy
  • 2015
  • Billable Thru Sept 30/2015
  • Non-Billable On/After Oct 1/2015

  • ICD-9-CM 359.1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 359.1 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
Convert to ICD-10-CM: 359.1 converts directly to:
  • 2015/16 ICD-10-CM G71.0 Muscular dystrophy
Approximate Synonyms
  • Distal muscular dystrophy
  • Duchenne muscular dystrophy
  • Emery Dreifuss muscular dystrophy
  • Emery-Dreifuss muscular dystrophy
  • Erbs muscular dystrophy
  • Erb's muscular dystrophy
  • Facioscapulohumeral muscular dystrophy
  • Kearns-Sayre syndrome (disorder)
  • Limb girdle muscular dystrophy
  • Limb-girdle muscular dystrophy
  • Mitochondrial myopathy, ocular
  • Mitochondrial ocular myopathy
  • Muscular dystrophy
  • Muscular dystrophy, distal
  • Muscular dystrophy, Duchenne
  • Muscular dystrophy, Emery Dreifuss
  • Muscular dystrophy, Erbs
  • Muscular dystrophy, facioscapulohumeral
  • Muscular dystrophy, hereditary progressive
  • Muscular dystrophy, limb girdle
  • Muscular dystrophy, neuropathic
  • Muscular dystrophy, ocular
  • Muscular dystrophy, oculopharyngeal
  • Neuropathic muscular dystrophy
  • Ocular muscular dystrophy
  • Oculopharyngeal muscular dystrophy
  • Restrictive lung disease due to muscular dystrophy
  • Restrictive lung mechanics due to muscular dystrophy
Clinical Information
  • A group of inherited progressive muscle disorders characterized by muscle weakness and eventual death of the muscle tissues. Examples include duchenne muscular dystrophy, becker's muscular dystrophy, emery-dreifuss muscular dystrophy, facioscapulohumeral muscular dystrophy, and limb-girdle muscular dystrophy
  • A heterogeneous group of inherited myopathies, characterized by wasting and weakness of the skeletal muscle. They are categorized by the sites of muscle weakness; age of onset; and inheritance patterns
  • A progressive disorder involving pelvic and scapular girdle muscles marked by weakness of proximal muscles of hip and shoulder areas with variable psychiatric disorders and occasional mild mental retardation. Type ia (lgmd1a) synonym: proximal limb-girdle muscular dystrophy type 1a a slowly progressive form of muscular dystrophy affecting the proximal limb muscles but sparing the face. (159000) type ib (lgmd1b) synonym: proximal limb-girdle muscular dystrophy type 1b a slowly progressive form of muscular dystrophy differing from lgmd1a by the nasal quality of speech. (omim 159001) type 2 (lgmd2, lgmd2a) synonyms: leyden-mobius syndrome distal muscular dystrophy pelvofemoral muscular dystrophy pelvofemoral syndrome tibial muscular dystrophy muscular dystrophy involving first the pelvic or, less commonly, shoulder girdle with occasional pseudohypertrophy of the calves with onset usually in childhood but sometimes in later stages of life. Muscle wasting tends to be asymmetric when the upper limbs are first involved. Progression of disease varies with inability to walk usually taking place at about 20 to 30 years of onset. Facial weakness and contractures may occur later. (omim 253600) type 3 (lgmd3, lgmd2b) a slowly progressive form of muscular dystrophy involving the pelvic girdle with onset in the late teens. (omim 253601)
  • An inherited disease where skeletal muscles are progressively weakened and wasted
  • General term for a group of inherited disorders which are characterized by progressive degeneration of skeletal muscles
  • Muscular dystrophy (md) refers to a group of more than 30 inherited diseases that cause muscle weakness and muscle loss. Some forms of md appear in infancy or childhood, while others may not appear until middle age or later. The different muscular dystrophies vary in who they affect and the symptoms. All forms of md grow worse as the person's muscles get weaker. Most people with md eventually lose the ability to walk. There is no cure for muscular dystrophy. Treatments include physical and speech therapy, orthopedic devices, surgery and medications. Some people with muscular dystrophy have mild cases that worsen slowly. Other cases are disabling and severe
  • Pelvic muscle weakness and atrophy associated with pseudohypertrophy of the calves. Two basic types are recognized: duchenne muscular dystrophy (type i) synonym: childhood pseudohypertrophic muscular dystrophy with the onset of symptoms between the ages of 3 and 5 years, the patients becoming bedridden by age of 12 and death by age 20 to 25 years. Becker muscular dystrophy (type ii) synonyms: adult pseudohypertrophic muscular dystrophy mild or benign x-linked recessive muscular dystrophy with onset of symptoms between the ages of 20 and 30 years and relatively normal life expectancy in most cases. Atrophic changes begin in the muscles of the pectoral girdle and trunk and extend to the extremities. As their size increases, the muscles become firm and resilient, but their strength diminishes and, eventually, atrophy ensues. Inability to rise to an upright position without turning to the side, waddling gait, and progressive weakness are the characteristic features. Pseudohypertrophy of the calf muscles is due to fibrous tissue and fat infiltration. Involvement of the heart consists of usually terminal cardiomyopathy. Fasciculation and atrophy of the tongue with dysphagia, dysarthria, and thickened nasal speech are usually associated. Usually mild and static mental retardation occurs in about 30% dmd patients most children having normal, even superior intelligence
  • X-linked recessive muscle disease caused by an inability to synthesize dystrophin, which is involved with maintaining the integrity of the sarcolemma; muscle fibers undergo a process that features degeneration and regeneration; clinical manifestations include proximal weakness in the first few years of life, pseudohypertrophy, cardiomyopathy and an increased incidence of impaired mentation; becker muscular dystrophy is a closely related condition featuring a later onset of disease (usually adolescence) and a slowly progressive course
Applies To
  • Muscular dystrophy:
    • NOS
    • distal
    • Duchenne
    • Erb's
    • fascioscapulohumeral
    • Gower's
    • Landouzy-Déjérine
    • limb-girdle
    • ocular
    • oculopharyngeal
ICD-9-CM Volume 2 Index entries containing back-references to 359.1:
  • Atrophy, atrophic
    • facioscapulohumeral (Landouzy-Déjérine) 359.1
    • Landouzy-Déjérine 359.1
    • pseudohypertrophic 359.1
  • Disease, diseased - see also Syndrome
    • Duchenne's 094.0
      • locomotor ataxia 094.0
      • muscular dystrophy 359.1
      • paralysis 335.22
      • pseudohypertrophy, muscles 359.1
    • Duchenne-Griesinger 359.1
    • Erb (-Landouzy) 359.1
  • Disorder - see also Disease
  • Duchenne's
    • disease 094.0
      • locomotor ataxia 094.0
      • muscular dystrophy 359.1
      • pseudohypertrophy, muscles 359.1
  • Duchenne-Griesinger disease 359.1
  • Dystrophy, dystrophia 783.9
    • Duchenne's 359.1
    • Erb's 359.1
    • Gowers' muscular 359.1
    • hereditary, progressive muscular 359.1
    • Landouzy-Déjérine 359.1
    • Leyden-Möbius 359.1
    • muscular 359.1
      • congenital (hereditary) 359.0
      • distal 359.1
      • Duchenne's 359.1
      • Erb's 359.1
      • fascioscapulohumeral 359.1
      • Gowers' 359.1
      • hereditary (progressive) 359.1
      • Landouzy-Déjérine 359.1
      • limb-girdle 359.1
      • myotonic 359.21
      • progressive (hereditary) 359.1
        • Charcôt-Marie-Tooth 356.1
      • pseudohypertrophic (infantile) 359.1
    • ocular 359.1
    • oculopharyngeal 359.1
    • pelvicrural atrophic 359.1
    • progressive ophthalmoplegic 359.1
    • scapuloperoneal 359.1
  • Erb's
    • disease 359.1
    • pseudohypertrophic muscular dystrophy 359.1
  • Facioscapulohumeral myopathy 359.1
  • Gowers'
    • muscular dystrophy 359.1
  • Hypertrophy, hypertrophic
    • pseudomuscular 359.1
  • Landouzy-Déjérine dystrophy (fascioscapulohumeral atrophy) 359.1
  • Leyden-Möbius dystrophy 359.1
  • Myopathy 359.9
    • distal 359.1
    • facioscapulohumeral 359.1
    • limb-girdle 359.1
    • ocular 359.1
    • oculopharyngeal 359.1
    • scapulohumeral 359.1
  • Ocular muscle - see also condition
    • myopathy 359.1
  • Paralysis, paralytic (complete) (incomplete) 344.9
    • muscle (flaccid) 359.9
      • due to nerve lesion NEC 355.9
      • eye (extrinsic) 378.55
      • iris sphincter 364.89
      • ischemic (complicating trauma) (Volkmann's) 958.6
      • pseudohypertrophic 359.1
    • pseudohypertrophic 359.1
      • muscle 359.1
  • Paresis (see also Paralysis) 344.9
    • pseudohypertrophic 359.1
  • Pseudohypertrophic muscular dystrophy (Erb's) 359.1
  • Pseudohypertrophy, muscle 359.1
  • Scapulohumeral myopathy 359.1
  • Syndrome - see also Disease
    • scapuloperoneal 359.1
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 359.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2015 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.