Specific code 2014 ICD-9-CM Diagnosis Code 710.1
Systemic sclerosis
  • Billable Code
  • ICD-9-CM 710.1 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 710.1 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Calcinosis, Raynaud's phenomenon, esophageal dysmotility, sclerodactyly, and telangiectasia (CREST) syndrome (disorder)
  • Crest syndrome
  • Lipodermatosclerosis
  • Lung disease with systemic sclerosis
  • Myopathy due to scleroderma (disorder)
  • Myopathy due to systemic sclerosis
  • Polyneuropathy due to systemic sclerosis
  • Progressive systemic sclerosis
  • Scleredema
  • Scleredema buschkes
  • Scleroderma
  • Scleroderma of lung
  • Scleroderma w glomerulonephritis
  • Scleroderma with glomerulonephritis
  • Scleroderma with glomerulonephritis (gn)
  • Systemic sclerosis induced by chemical, including drug
  • Systemic sclerosis induced by chemical, including drugs
  • Systemic sclerosis induced by drugs and chemicals
  • Systemic sclerosis w myopathy
  • Systemic sclerosis w polyneuropathy
Clinical Information
  • A chronic disorder marked by hardening and thickening of the skin. Scleroderma can be localized or it can affect the entire body (systemic).
  • A chronic disorder, possibly autoimmune, marked by excessive production of collagen which results in hardening and thickening of body tissues. The two types of systemic scleroderma, limited cutaneous and diffuse cutaneous are classified with focus on the extent of affected skin. A relationship exists between the extent of skin area affected and degree of internal organ/system involvement. Systemic scleroderma can manifest itself in pulmonary fibrosis, raynaud's syndrome, digestive system telangiectasias, renal hypertension and/or pulmonary hypertension.
  • A chronic multi-system disorder of connective tissue. It is characterized by sclerosis in the skin, the lungs, the heart, the gastrointestinal tract, the kidneys, and the musculoskeletal system. Other important features include diseased small blood vessels and autoantibodies. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: limited scleroderma and diffuse scleroderma.
  • A disease that is marked by hardening and thickening of skin, connective tissue that surrounds other tissues and organs, and blood vessels.
  • A rare, chronic disease characterized by excessive deposits of collagen in the skin or other organs
  • Chronic hardening and thickening of the skin caused by swelling and thickening of fibrous tissue leading to eventual atrophy of the epidermis; can occur as a localized or a systemic disease.
  • Systemic disorder of the connective tissue; manifested by hardening and thickening of the skin, by abnormalities involving the microvasculature and larger vessels, and by fibrotic degenerative changes in various body organs including the heart, lungs, kidneys, and gastrointestinal tract.
710.1 Excludes
  • circumscribed scleroderma (701.0)
Applies To
  • Acrosclerosis
  • CRST syndrome
  • Progressive systemic sclerosis
  • Scleroderma
Use Additional
  • Use additional code to identify manifestation, as:
Convert to ICD-10-CM: 710.1 converts approximately to:
  • 2014 ICD-10-CM M34.0 Progressive systemic sclerosis
    Or:
  • 2014 ICD-10-CM M34.1 CR(E)ST syndrome
    Or:
  • 2014 ICD-10-CM M34.9 Systemic sclerosis, unspecified
ICD-9-CM Volume 2 Index entries containing back-references to 710.1:
  • Acroscleriasis (see also Scleroderma) 710.1
  • Acroscleroderma (see also Scleroderma) 710.1
  • Acrosclerosis (see also Scleroderma) 710.1
  • Buschke's disease or scleredema (adultorum) 710.1
  • Calcinosis (generalized) (interstitial) (tumoral) (universalis) 275.49
    • Raynaud's phenomenonsclerodactylytelangiectasis (CRST) 710.1
  • Chorionitis (see also Scleroderma) 710.1
  • CRST syndrome (cutaneous systemic sclerosis) 710.1
  • Dermatosclerosis (see also Scleroderma) 710.1
  • Disease, diseased - see also Syndrome
    • Buschke's 710.1
  • Scleredema
    • adultorum 710.1
    • Buschke's 710.1
  • Sclerema
    • adultorum 710.1
  • Scleroderma, sclerodermia (acrosclerotic) (diffuse) (generalized) (progressive) (pulmonary) 710.1
  • Sclerosis, sclerotic
    • progressive systemic 710.1
    • systemic (progressive) 710.1
      • with lung involvement 710.1 [517.2]
  • Syndrome - see also Disease
    • CRST (cutaneous systemic sclerosis) 710.1
    • Thibierge-Weissenbach (cutaneous systemic sclerosis) 710.1
    • Weissenbach-Thibierge (cutaneous systemic sclerosis) 710.1
  • Thibierge-Weissenbach syndrome (cutaneous systemic sclerosis) 710.1
  • Trophoneurosis NEC 356.9
    • disseminated 710.1
  • Weissenbach-Thibierge syndrome (cutaneous systemic sclerosis) 710.1
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 710.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.