Non-specific code 2014 ICD-9-CM Diagnosis Code 345.6
Infantile spasms
  • Non-Billable Code
  • There are 2 ICD-9-CM codes below 345.6 that define this diagnosis in greater detail. Do not use this code on a reimbursement claim.
Clinical Information
  • A rare autosomal recessive inherited neurodegenerative disorder caused by mutations in the pla2g6 gene. It is characterized by the development of swellings called spheroids along the axons of the central nervous system. Signs and symptoms appear early in life and include movement difficulties, muscle hypotonia and spasticity, and dementia.
  • An epileptic syndrome characterized by the triad of infantile spasms, hypsarrhythmia, and arrest of psychomotor development at seizure onset. The majority present between 3-12 months of age, with spasms consisting of combinations of brief flexor or extensor movements of the head, trunk, and limbs. The condition is divided into two forms: cryptogenic (idiopathic) and symptomatic (secondary to a known disease process such as intrauterine infections; nervous system abnormalities; brain diseases, metabolic, inborn; prematurity; perinatal asphyxia; tuberous sclerosis; etc.). (from menkes, textbook of child neurology, 5th ed, pp744-8)
  • Myoclonus epilepsy of infancy and early childhood, characterized by seizures involving the muscles of the neck, trunk, and limbs, and manifested by nodding of the head and flexion of the arms. The seizures are associated with brain abnormalities and frequent mental retardation.
345.6 Excludes
Applies To
  • Hypsarrhythmia
  • Lightning spasms
  • Salaam attacks
ICD-9-CM Volume 2 Index entries containing back-references to 345.6:
  • Attack
    • salaam (see also Epilepsy) 345.6
  • Contraction, contracture, contracted
    • infantile (see also Epilepsy) 345.6
  • Convulsions (idiopathic) 780.39
    • salaam (see also Epilepsy) 345.6
  • Hypsarrhythmia (see also Epilepsy) 345.6
  • Seizure(s) 780.39
    • salaam (see also Epilepsy) 345.6
  • Spasm, spastic, spasticity (see also condition) 781.0
    • infantile (see also Epilepsy) 345.6
    • lightning (see also Epilepsy) 345.6
    • nodding 307.3
      • infantile (see also Epilepsy) 345.6
    • salaam (infantile) (see also Epilepsy) 345.6
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 345.6 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.