Specific code 2014 ICD-9-CM Diagnosis Code 288.01
Congenital neutropenia
  • Billable Code
  • ICD-9-CM 288.01 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 288.01 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Neutropenia, congenital
Clinical Information
  • A rare disorder characterized by recurrent infantile infections and absence of neutrophils in the peripheral blood.
  • An inherited disorder in which there is a lower-than-normal number of neutrophils (a type of white blood cell that is important in fighting infections). Infants with the disorder get infections caused by bacteria, and are at an increased risk of acute myelogenous leukemia (aml) or myelodysplasia (a bone marrow disorder).
Applies To
  • Congenital agranulocytosis
  • Infantile genetic agranulocytosis
  • Kostmann's syndrome
Convert to ICD-10-CM: 288.01 converts directly to:
  • 2014 ICD-10-CM D70.0 Congenital agranulocytosis
ICD-9-CM Volume 2 Index entries containing back-references to 288.01:
  • Agranulocytosis (see also Neutropenia) 288.09
    • genetic 288.01
    • infantile 288.01
  • Disease, diseased - see also Syndrome
    • Kostmann's (infantile genetic agranulocytosis) 288.01
  • Kostmann's disease or syndrome (infantile genetic agranulocytosis) 288.01
  • Neutropenia, neutropenic (idiopathic) (pernicious) (primary) 288.00
    • congenital (nontransient) 288.01
    • genetic 288.01
    • infantile 288.01
  • Syndrome - see also Disease
    • Kostmann's (infantile genetic agranulocytosis) 288.01
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 288.01 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.