Specific code 2014 ICD-9-CM Diagnosis Code 284.09
Other constitutional aplastic anemia
  • Billable Code
  • Short description: Const aplastc anemia NEC.
  • ICD-9-CM 284.09 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 284.09 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Acquired Fanconi syndrome
  • Anemia, Fanconi
  • Congenital hypoplastic anemia
  • Constitutional aplastic anemia
  • Constitutional aplastic anemia with malformation
  • Constitutional red cell aplasia and hypoplasia
  • Erythrogenesis imperfecta
  • Estren-Dameshek anemia
  • Fanconi anemia
  • Fanconi's anemia
Clinical Information
  • A rare and often fatal inherited disease in which the bone marrow fails to produce red blood cells, white blood cells, platelets, or a combination of these cells. The disease may transform into myelodysplastic syndrome or leukemia.
  • Fanconi anemia (fa) is an autosomal recessive genetic disorder characterised clinically by progressive bone marrow failure, skeletal deformities and a predisposition to neoplasia. Patient cells manifest an extreme chromosomal instability and hypersensitivity to polyfunctional alkylating agents. It is assumed that the basic defect is related to the repair of dna damage, in particular that of so-called dna crosslinks. Currently there are eight complementation groups in fa (fa-a-fa-h) which indicates that at least eight independent genes can lead to fa. Three of these genes have been identified: fanca, fancc and fancg. (from pmid 10472548)
Applies To
  • Fanconi's anemia
  • Pancytopenia with malformations
Convert to ICD-10-CM: 284.09 converts directly to:
  • 2014 ICD-10-CM D61.09 Other constitutional aplastic anemia
ICD-9-CM Volume 2 Index entries containing back-references to 284.09:
  • Absence (organ or part) (complete or partial)
  • Aleukia
  • Anemia 285.9
    • Fanconi's (congenital pancytopenia) 284.09
  • Disease, diseased - see also Syndrome
    • Fanconi's (congenital pancytopenia) 284.09
  • Erythrogenesis imperfecta 284.09
  • Failure, failed
    • bone marrow (anemia) 284.9
      • acquired (secondary) 284.89
      • congenital 284.09
      • idiopathic 284.9
  • Fanconi's anemia (congenital pancytopenia) 284.09
  • Hypoplasia, hypoplasis 759.89
  • Pancytopenia (acquired) 284.19
    • with
      • malformations 284.09
      • myelodysplastic syndrome - see Syndrome, myelodysplastic
    • congenital 284.09
  • Panhematopenia 284.81
    • congenital 284.09
    • constitutional 284.09
  • Panhemocytopenia 284.81
    • congenital 284.09
    • constitutional 284.09
  • Panmyelopathy, familial constitutional 284.09
  • Syndrome - see also Disease
    • Fanconi's (anemia) (congenital pancytopenia) 284.09
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 284.09 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.