Specific code 2014 ICD-9-CM Diagnosis Code 277.6
Other deficiencies of circulating enzymes
  • Billable Code
  • Short description: Defic circul enzyme NEC.
  • ICD-9-CM 277.6 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 277.6 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • 6-Pyruvoyl-tetrahydrobiopterin synthase deficiency
  • Acetyl-CoA: carboxylase deficiency
  • Acid phosphatase deficiency
  • Alpha-2-antitrypsin deficiency
  • Angioedema, hereditary
  • Beta ketothiolase deficiency
  • Bifunctional peroxisomal enzyme deficiency
  • Biotinidase deficiency
  • Circulating enzyme deficiency
  • Clinical manifestation of carnosinase deficiency
  • Clinical manifestation of enzyme deficiency
  • Combined deficiency of sialidase AND beta galactosidase
  • Complex V deficiency
  • Cytochrome p450 CYP1A2 enzyme deficiency
  • Cytochrome p450 CYP2C19 enzyme deficiency
  • Cytochrome p450 CYP2C9 enzyme deficiency
  • Cytochrome p450 CYP2D6 enzyme deficiency
  • Cytochrome p450 CYP2E1 enzyme deficiency
  • Cytochrome p450 CYP3A enzyme deficiency
  • Cytochrome p450 enzyme deficiency
  • Deficiency of 1,3-beta-glucan synthase
  • Deficiency of 1,4-alpha-glucan 6alpha-glucosyltransferase
  • Deficiency of 1,4-alpha-glucan branching enzyme
  • Deficiency of 2,4-dienoyl-CoA reductase
  • Deficiency of 2,5-diaminovalerate aminotransferase
  • Deficiency of -20-hydroxysteroid dehydrogenase
  • Deficiency of -2-hydroxy-acid oxidase
  • Deficiency of 2-hydroxyglutarate dehydrogenase
  • Deficiency of 2-methylbutyryl-CoA dehydrogenase
  • Deficiency of 3alpha-hydroxycholanate dehydrogenase
  • Deficiency of 3alpha-hydroxysteroid dehydrogenase
  • Deficiency of 3-hydroxyacyl-CoA dehydrogenase
  • Deficiency of 3-hydroxybutyrate dehydrogenase
  • Deficiency of 3-hydroxybutyryl-CoA epimerase
  • Deficiency of 3-hydroxyisobutyrate dehydrogenase
  • Deficiency of 3-hydroxyisobutyryl CoA hydrolase
  • Deficiency of 3-mercaptopyruvate sulfurtransferase
  • Deficiency of 3'-nucleotidase
  • Deficiency of 3-oxoacid CoA-transferase
  • Deficiency of 3-oxoadipate CoA-transferase
  • Deficiency of 4-hydroxy-2-oxoglutarate aldolase
  • Deficiency of 5'-nucleotidase
  • Deficiency of 6-phosphofructokinase
  • Deficiency of A-ase
  • Deficiency of acetate kinase
  • Deficiency of acetate-CoA ligase
  • Deficiency of acetoacetyl-CoA reductase
  • Deficiency of acetylcholinesterase
  • Deficiency of acetyl-CoA acetyltransferase
  • Deficiency of acetyl-CoA acylase
  • Deficiency of acetyl-CoA acyltransferase
  • Deficiency of acetyl-CoA deacylase
  • Deficiency of acetyl-CoA hydrolase
  • Deficiency of acetylesterase
  • Deficiency of acetylserotonin methyltransferase
  • Deficiency of acid-aminoacid ligase
  • Deficiency of acid-ammonia ligase
  • Deficiency of aconitate hydratase
  • Deficiency of acylphosphatase
  • Deficiency of adenine deaminase
  • Deficiency of adenine phosphoribosyltransferase
  • Deficiency of adenosine kinase
  • Deficiency of adenosinetriphosphatase
  • Deficiency of adenosylhomocysteinase
  • Deficiency of adenylate kinase
  • Deficiency of adenylylsulfate kinase
  • Deficiency of ADP deaminase
  • Deficiency of alanine aminotransferase
  • Deficiency of alanine dehydrogenase
  • Deficiency of alanine-oxo-acid aminotransferase
  • Deficiency of alanine-tRNA ligase
  • Deficiency of alcohol sulfotransferase
  • Deficiency of aldehyde dehydrogenase
  • Deficiency of aldehyde oxidase
  • Deficiency of aldehyde reductase
  • Deficiency of aldehyde-lyase
  • Deficiency of aldonolactonase
  • Deficiency of aldose 1-epimerase
  • Deficiency of alkaline phosphatase
  • Deficiency of alkaline phosphomonoesterase
  • Deficiency of alkylhalidase
  • Deficiency of allantoicase
  • Deficiency of allantoinase
  • Deficiency of alpha- and beta-trypsin
  • Deficiency of alpha-1,4-glucan-protein synthase
  • Deficiency of alpha-aminoacylpeptide hydrolase
  • Deficiency of alpha-amylase
  • Deficiency of alpha-galactosidase
  • Deficiency of alpha-glucosidase
  • Deficiency of amidase
  • Deficiency of amidinotransferase
  • Deficiency of amidophosphoribosyltransferase
  • Deficiency of amine oxidase
  • Deficiency of aminoacyl-histidine dipeptidase
  • Deficiency of aminoacyltransferase
  • Deficiency of aminopeptidase
  • Deficiency of aminotransferase
  • Deficiency of ammonia-lyase
  • Deficiency of AMP deaminase
  • Deficiency of AMP nucleosidase
  • Deficiency of amylase
  • Deficiency of amylo-1,6-glucosidase
  • Deficiency of arginine deiminase
  • Deficiency of aromatic-L-amino-acid decarboxylase
  • Deficiency of aryl sulfotransferase
  • Deficiency of arylamine acetyltransferase
  • Deficiency of arylesterase
  • Deficiency of arylsulfatase
  • Deficiency of asparagine-oxo-acid aminotransferase
  • Deficiency of aspartate 4-decarboxylase
  • Deficiency of aspartate aminotransferase
  • Deficiency of aspartate carbamoyltransferase
  • Deficiency of aspartate kinase
  • Deficiency of aspartic proteinase
  • Deficiency of ATP pyrophosphatase
  • Deficiency of azobenzene reductase
  • Deficiency of benzaldehyde dehydrogenase
  • Deficiency of benzoylcholinesterase
  • Deficiency of beta-amylase
  • Deficiency of beta-fructofuranosidase
  • Deficiency of beta-galactosidase
  • Deficiency of beta-glucosidase
  • Deficiency of beta-glucuronidase
  • Deficiency of betaine-aldehyde dehydrogenase
  • Deficiency of betaine-homocysteine methyltransferase
  • Deficiency of beta-ureidopropionase
  • Deficiency of bisphosphoglycerate mutase
  • Deficiency of bisphosphoglycerate phosphatase
  • Deficiency of butyrate-acetoacetate CoA-transferase
  • Deficiency of butyrylcholine esterase
  • Deficiency of carbamate kinase
  • Deficiency of carbonate dehydratase
  • Deficiency of carbon-carbon lyase
  • Deficiency of carbon-halide lyase
  • Deficiency of carbon-nitrogen lyase
  • Deficiency of carbon-oxygen lyase
  • Deficiency of carbon-sulfur lyase
  • Deficiency of carboxylesterase
  • Deficiency of carboxylic ester hydrolase
  • Deficiency of carboxy-lyase
  • Deficiency of carboxypeptidase A
  • Deficiency of carboxypeptidase B
  • Deficiency of carnitine acetyltransferase
  • Deficiency of carnosinase
  • Deficiency of catalase
  • Deficiency of catechol oxidase
  • Deficiency of cathepsin C
  • Deficiency of cellulase
  • Deficiency of chlorophyllase
  • Deficiency of cholate-CoA ligase
  • Deficiency of cholesterol esterase
  • Deficiency of cholesterol oxidase
  • Deficiency of choline acetyltransferase
  • Deficiency of choline dehydrogenase
  • Deficiency of choline esterase I
  • Deficiency of choline esterase II
  • Deficiency of choline kinase
  • Deficiency of choline-phosphate cytidylyltransferase
  • Deficiency of cholinephosphotransferase
  • Deficiency of cholinesterase
  • Deficiency of chymosin
  • Deficiency of chymotrypsin
  • Deficiency of chymotrypsin A and B
  • Deficiency of circulating enzyme
  • Deficiency of citrate-synthase
  • Deficiency of coenzyme-A transferase
  • Deficiency of creatine kinase
  • Deficiency of cysteamine dioxygenase
  • Deficiency of cysteine aminotransferase
  • Deficiency of cysteine carboxypeptidase
  • Deficiency of cysteine proteinase
  • Deficiency of cysteinyl-glycine dipeptidase
  • Deficiency of cystine reductase
  • Deficiency of cytidine deaminase
  • Deficiency of cytochrome-b>5< reductase
  • Deficiency of cytochrome-c peroxidase
  • Deficiency of cytosol aminopeptidase
  • Deficiency of D-2-hydroxy-acid dehydrogenase
  • Deficiency of D-amino-acid oxidase
  • Deficiency of D-aspartate oxidase
  • Deficiency of dehydrogenase
  • Deficiency of dehydrogluconate dehydrogenase
  • Deficiency of dehydrogluconokinase
  • Deficiency of deoxyribonuclease I
  • Deficiency of deoxyribonuclease II
  • Deficiency of dephospho-CoA kinase
  • Deficiency of dextranase
  • Deficiency of dihydrolipoamide acetyltransferase
  • Deficiency of dihydroorotase
  • Deficiency of dihydrouracil dehydrogenase
  • Deficiency of diisopropyl-fluorophosphatase
  • Deficiency of dimethylallyltranstransferase
  • Deficiency of dioxygenase
  • Deficiency of dipeptidase
  • Deficiency of dipeptide hydrolase
  • Deficiency of dipeptidyl peptidase I
  • Deficiency of dipeptidyl-amino-peptidase I
  • Deficiency of dipeptidylpeptide hydrolase
  • Deficiency of diphosphomevalonate decarboxylase
  • Deficiency of diphosphoric monoester hydrolase
  • Deficiency of D-lactate dehydrogenase
  • Deficiency of DNA nucleotidylexotransferase
  • Deficiency of DNA-directed DNA polymerase
  • Deficiency of DNA-directed RNA polymerase
  • Deficiency of endo-1,3-beta-glucanase
  • Deficiency of endopeptidase
  • Deficiency of endoribonuclease
  • Deficiency of enolase
  • Deficiency of enoyl-CoA hydratase
  • Deficiency of enteropeptidase
  • Deficiency of epimerase
  • Deficiency of erythritol kinase
  • Deficiency of estradiol 6beta-monooxygenase
  • Deficiency of ethanolamine-phosphate cytidylyltransferase
  • Deficiency of ethanolaminephosphotransferase
  • Deficiency of ether hydrolase
  • Deficiency of exoribonuclease
  • Deficiency of ferroxidase
  • Deficiency of FMN adenylyltransferase
  • Deficiency of formaldehyde dehydrogenase
  • Deficiency of formamidase
  • Deficiency of formate dehydrogenase
  • Deficiency of formate-tetrahydrofolate ligase
  • Deficiency of formiminotetrahydrofolate cyclodeaminase
  • Deficiency of formyltetrahydrofolate deformylase
  • Deficiency of fructose-bisphosphatase
  • Deficiency of fructose-bisphosphate aldolase
  • Deficiency of fumarate hydratase
  • Deficiency of fumarylacetoacetase
  • Deficiency of galactonolactone dehydrogenase
  • Deficiency of galactose dehydrogenase
  • Deficiency of gentisate l,2-dioxygenase
  • Deficiency of glucan 1,3-alpha-glucosidase
  • Deficiency of glucan 1,4-alpha-glucosidase
  • Deficiency of glucokinase
  • Deficiency of gluconate 2-dehydrogenase
  • Deficiency of gluconokinase
  • Deficiency of gluconolactonase
  • Deficiency of glucosamine acetyltransferase
  • Deficiency of glucosamine kinase
  • Deficiency of glucosamine-6-phosphate isomerase
  • Deficiency of glucosamine-phosphate acetyltransferase
  • Deficiency of glucose dehydrogenase
  • Deficiency of glucose oxidase
  • Deficiency of glucose-1-phosphatase
  • Deficiency of glucose-1-phosphate phosphodismutase
  • Deficiency of glucose-6-phosphate dehydrogenase
  • Deficiency of glutamate decarboxylase
  • Deficiency of glutamate dehydrogenase
  • Deficiency of glutamate-ammonia ligase
  • Deficiency of glutaminase
  • Deficiency of glutamine phenylacetyltransferase
  • Deficiency of glutamine-fructose-6-phosphate aminotransferase
  • Deficiency of glutamine-pyruvate aminotransferase
  • Deficiency of glutarate-CoA ligase
  • Deficiency of glutathione reductase H)
  • Deficiency of glutathione synthase
  • Deficiency of glutathione thiolesterase
  • Deficiency of glutathione-homocystine transhydrogenase
  • Deficiency of glyceraldehyde-3-phosphate dehydrogenase
  • Deficiency of glycerate kinase
  • Deficiency of glycerol kinase
  • Deficiency of glycerol-3-phosphate acyltransferase
  • Deficiency of glycerophosphatase
  • Deficiency of glycerophosphocholine phosphodiesterase
  • Deficiency of glycine acyltransferase
  • Deficiency of glycine amidinotransferase
  • Deficiency of glycine formiminotransferase
  • Deficiency of glycine hydroxymethyltransferase
  • Deficiency of glycosulfatase
  • Deficiency of glycosyltransferase
  • Deficiency of GMP synthase
  • Deficiency of guanidinoacetate kinase
  • Deficiency of guanidinoacetate methyltransferase
  • Deficiency of guanine deaminase
  • Deficiency of heparin lyase
  • Deficiency of hexokinase
  • Deficiency of hexose oxidase
  • Deficiency of hexosyltransferase
  • Deficiency of histidine ammonia-lyase
  • Deficiency of histidine decarboxylase
  • Deficiency of histidinol dehydrogenase
  • Deficiency of homocysteine desulfhydrase
  • Deficiency of homoserine kinase
  • Deficiency of hyaluronate lyase
  • Deficiency of hyaluronoglucosaminidase
  • Deficiency of hydrogen-sulfide acetyltransferase
  • Deficiency of hydrolase
  • Deficiency of hydrolyase
  • Deficiency of hydroxyacylglutathione hydrolase
  • Deficiency of hydroxyalkyl-protein kinase
  • Deficiency of hydroxymethylglutaryl-CoA hydrolase
  • Deficiency of hydroxymethylglutaryl-CoA lyase
  • Deficiency of hydroxymethylglutaryl-CoA reductase
  • Deficiency of hydroxymethylglutaryl-CoA synthase
  • Deficiency of hypoxanthine phosphoribosyltransferase
  • Deficiency of imidodipeptidase
  • Deficiency of iminodipeptidase
  • Deficiency of IMP cyclohydrolase
  • Deficiency of IMP dehydrogenase
  • Deficiency of inorganic pyrophosphatase
  • Deficiency of inosinase
  • Deficiency of inosine nucleosidase
  • Deficiency of iodide peroxidase
  • Deficiency of isocitrate dehydrogenase
  • Deficiency of isocitrate lyase
  • Deficiency of isoleucine-tRNA ligase
  • Deficiency of isomerase
  • Deficiency of isopentenyl-diphosphate delta-isomerase
  • Deficiency of ketohexokinase
  • Deficiency of ketotetrose-phosphate aldolase
  • Deficiency of kynurenine 3-monooxygenase
  • Deficiency of kynurenine-oxoglutarate aminotransferase
  • Deficiency of lactate racemase
  • Deficiency of lactonase
  • Deficiency of lactoylglutathione lyase
  • Deficiency of L-amino-acid oxidase
  • Deficiency of L-arabinose dehydrogenase
  • Deficiency of L-asparagine amidohydrolase
  • Deficiency of lecithinase D
  • Deficiency of leucine aminopeptidase
  • Deficiency of leucine aminotransferase
  • Deficiency of leucine-tRNA ligase
  • Deficiency of L-gulonate dehydrogenase
  • Deficiency of lichenase
  • Deficiency of ligase
  • Deficiency of lipophosphodiesterase II
  • Deficiency of L-lactate dehydrogenase
  • Deficiency of long-chain fatty-acyl-CoA hydrolase
  • Deficiency of long-chain-fatty-acid-CoA ligase
  • Deficiency of L-prolylglycine dipeptidase
  • Deficiency of L-serine dehydratase
  • Deficiency of lyase
  • Deficiency of lysine racemase
  • Deficiency of lysine-tRNA ligase
  • Deficiency of lysolecithin acylmutase
  • Deficiency of lysophospholipase
  • Deficiency of lysozyme
  • Deficiency of malate dehydrogenase
  • Deficiency of malate oxidase
  • Deficiency of maleylacetoacetate isomerase
  • Deficiency of malonate CoA-transferase
  • Deficiency of malonyl-CoA decarboxylase
  • Deficiency of maltose phosphorylase
  • Deficiency of mannitol dehydrogenase
  • Deficiency of mannokinase
  • Deficiency of mannose-6-phosphate isomerase
  • Deficiency of metallocarboxypeptidase
  • Deficiency of metalloproteinase
  • Deficiency of methenyltetrahydrofolate cyclohydrolase
  • Deficiency of methionine adenosyltransferase
  • Deficiency of methionine-tRNA ligase
  • Deficiency of methylaspartate mutase
  • Deficiency of methylcrotonoyl-CoA carboxylase
  • Deficiency of methylenetetrahydrofolate dehydrogenase
  • Deficiency of methylglutaconyl-CoA hydratase
  • Deficiency of methylmalonyl-CoA mutase
  • Deficiency of methyltransferase
  • Deficiency of mevaldate reductase
  • Deficiency of mevalonate kinase
  • Deficiency of monodehydroascorbate reductase
  • Deficiency of monooxygenase
  • Deficiency of mutase
  • Deficiency of myo-inositol oxygenase
  • Deficiency of N-acetyl-beta-glucosaminidase
  • Deficiency of N-acetylneuraminate lyase
  • Deficiency of NAD^+^ kinase
  • Deficiency of NAD^+^ nucleosidase
  • Deficiency of NAD^+^ synthase
  • Deficiency of NAD^+^ transhydrogenase
  • Deficiency of NADase
  • Deficiency of NADH dehydrogenase
  • Deficiency of NADPH-ferrihemoprotein reductase
  • Deficiency of NAPH cytochrome-c>2< reductase
  • Deficiency of nicotinamide methyltransferase
  • Deficiency of nicotinamide phosphoribosyltransferase
  • Deficiency of nicotinamide-nucleotide adenylyltransferase
  • Deficiency of nicotinate dehydrogenase
  • Deficiency of nicotinate phosphoribosyltransferase
  • Deficiency of nitrate reductase
  • Deficiency of N-methyl-L-amino-acid oxidase
  • Deficiency of non-specific cholinesterase
  • Deficiency of nucleosidase
  • Deficiency of nucleoside-diphosphatase
  • Deficiency of nucleoside-diphosphate kinase
  • Deficiency of nucleoside-phosphate kinase
  • Deficiency of nucleotidase
  • Deficiency of nucleotide pyrophosphatase
  • Deficiency of nucleotidyltransferase
  • Deficiency of O-acetylserine -lyase
  • Deficiency of omega peptidase
  • Deficiency of orotate phosphoribosyltransferase
  • Deficiency of oxalate CoA-transferase
  • Deficiency of oxidase
  • Deficiency of oximinotransferase
  • Deficiency of oxo-acid-lyase
  • Deficiency of oxoglutarate dehydrogenase
  • Deficiency of oxygenase
  • Deficiency of palmitoyl-CoA hydrolase
  • Deficiency of pancreatic elastase
  • Deficiency of pantetheine kinase
  • Deficiency of pantetheine-phosphate adenylyltransferase
  • Deficiency of pantothenoylcysteine decarboxylase
  • Deficiency of pectin methoxylase
  • Deficiency of pectin methylesterase
  • Deficiency of pectinesterase
  • Deficiency of pentosyltransferase
  • Deficiency of pepsin A
  • Deficiency of pepsin B
  • Deficiency of peptidase a
  • Deficiency of peptide hydrolase
  • Deficiency of peptidoglycan endopeptidase
  • Deficiency of peroxidase
  • Deficiency of phenylalanine 4-monooxygenase
  • Deficiency of phenylpyruvate tautomerase
  • Deficiency of phosphatase
  • Deficiency of phosphatidate phosphatase
  • Deficiency of phosphoacetylglucosamine mutase
  • Deficiency of phosphoadenylate 3'-nucleotidase
  • Deficiency of phosphoamidase
  • Deficiency of phosphoglucokinase
  • Deficiency of phosphogluconate dehydrogenase
  • Deficiency of phosphoglycerate kinase
  • Deficiency of phosphoglycerate mutase
  • Deficiency of phosphoketolase
  • Deficiency of phospholipase A>2<
  • Deficiency of phospholipase C
  • Deficiency of phospholipase D
  • Deficiency of phosphomevalonate kinase
  • Deficiency of phosphomonoesterase
  • Deficiency of phosphopantothenate-cysteine ligase
  • Deficiency of phosphoprotein phosphatase
  • Deficiency of phosphoribokinase
  • Deficiency of phosphoribosylamine-glycine ligase
  • Deficiency of phosphoribosylaminoimidazole carboxylase
  • Deficiency of phosphoribosylaminoimidazolecarboxamide formyltransferase
  • Deficiency of phosphoribosylaminoimidazole-succinocarboxamide synthase
  • Deficiency of phosphoribosylformylglycinamidine cyclo-ligase
  • Deficiency of phosphoribosylformylglycinamidine synthase
  • Deficiency of phosphoribosylglycinamide formyltransferase
  • Deficiency of phosphoric diester hydrolase
  • Deficiency of phosphoric monoester hydrolase
  • Deficiency of phosphorus-oxygen lyase
  • Deficiency of phosphorylase phosphatase
  • Deficiency of phosphoserine phosphatase
  • Deficiency of phosphotransferase
  • Deficiency of plasmin
  • Deficiency of polygalacturonase
  • Deficiency of polyribonucleotide nucleotidyltransferase
  • Deficiency of progesterone 11alpha-monooxygenase
  • Deficiency of prolidase
  • Deficiency of prolinase
  • Deficiency of proline dipeptidase
  • Deficiency of prolyl dipeptidase
  • Deficiency of propionyl-CoA carboxylase
  • Deficiency of protein kinase
  • Deficiency of protocatechuate 3,4-dioxygenase
  • Deficiency of pyridoxal kinase
  • Deficiency of pyridoxamine-phosphate oxidase
  • Deficiency of pyrophosphotransferase
  • Deficiency of pyrroline-2-carboxylate reductase
  • Deficiency of pyrroline-5-carboxylate reductase
  • Deficiency of pyruvate decarboxylase
  • Deficiency of quinate dehydrogenase
  • Deficiency of racemase
  • Deficiency of reductase
  • Deficiency of renin
  • Deficiency of retinal isomerase
  • Deficiency of retinyl-palmitate esterase
  • Deficiency of rhamnulokinase
  • Deficiency of riboflavin kinase
  • Deficiency of ribokinase
  • Deficiency of ribonuclease
  • Deficiency of ribose-5-phosphate isomerase
  • Deficiency of ribose-phosphate pyrophosphokinase
  • Deficiency of ribosomal cathepsin
  • Deficiency of ribosomal neutral proteinase
  • Deficiency of ribosylnicotinamide kinase
  • Deficiency of ribulokinase
  • Deficiency of ribulose-phosphate 3-epimerase
  • Deficiency of sarcosine oxidase
  • Deficiency of sedoheptulokinase
  • Deficiency of serine carboxypeptidase
  • Deficiency of serine proteinase
  • Deficiency of serine-tRNA ligase
  • Deficiency of shikimate dehydrogenase
  • Deficiency of sialidase
  • Deficiency of squalene monooxygenase
  • Deficiency of steroid 11-beta-monooxygenase
  • Deficiency of steroid 17-alpha-monooxygenase
  • Deficiency of steroid 21-monooxygenase
  • Deficiency of steroid delta-isomerase
  • Deficiency of succinate dehydrogenase
  • Deficiency of succinate-CoA ligase
  • Deficiency of succinyl-CoA hydrolase
  • Deficiency of sulfatase
  • Deficiency of sulfate adenylyltransferase
  • Deficiency of sulfinoalanine decarboxylase
  • Deficiency of sulfite reductase
  • Deficiency of sulfotransferase
  • Deficiency of sulfuric ester hydrolase
  • Deficiency of sulfurtransferase
  • Deficiency of tannase
  • Deficiency of thetin-homocysteine methyltransferase
  • Deficiency of thiamin pyridinylase
  • Deficiency of thiamin pyrophosphokinase
  • Deficiency of thioethanolamine acetyltransferase
  • Deficiency of thioether hydrolase
  • Deficiency of thiolester hydrolase
  • Deficiency of thiosulfate sulfurtransferase
  • Deficiency of threonine aldolase
  • Deficiency of threonine dehydratase
  • Deficiency of threonine-tRNA ligase
  • Deficiency of thymidine phosphorylase
  • Deficiency of transacylase
  • Deficiency of transaldolase
  • Deficiency of transcarbamoylase
  • Deficiency of transcarboxylase
  • Deficiency of transferase
  • Deficiency of transformiminase
  • Deficiency of transformylase
  • Deficiency of transhydroxymethylase
  • Deficiency of transketolase
  • Deficiency of triacylglycerol lipase
  • Deficiency of trimetaphosphatase
  • Deficiency of triokinase
  • Deficiency of tripeptide aminopeptidase
  • Deficiency of triphosphoric monoester hydrolase
  • Deficiency of tropinesterase
  • Deficiency of true cholinesterase
  • Deficiency of trypsin
  • Deficiency of tryptophan 2,3-dioxygenase
  • Deficiency of tryptophan 5-monooxygenase
  • Deficiency of tryptophan-tRNA ligase
  • Deficiency of tyraminase
  • Deficiency of tyrosine aminotransferase
  • Deficiency of tyrosine decarboxylase
  • Deficiency of tyrosine-tRNA ligase
  • Deficiency of UDPglucose dehydrogenase
  • Deficiency of UDPglucose-hexose-1-phosphate uridylyltransferase
  • Deficiency of unspecific monooxygenase
  • Deficiency of uracil dehydrogenase
  • Deficiency of uracil phosphoribosyltransferase
  • Deficiency of urate oxidase
  • Deficiency of urease
  • Deficiency of uridine phosphorylase
  • Deficiency of uronolactonase
  • Deficiency of UTP-glucose-1-phosphate uridylyltransferase
  • Deficiency of valine-tRNA ligase
  • Deficiency of w-amidase
  • Deficiency of xanthine oxidase
  • Deficiency of xylan endo-1,3-beta-xylosidase
  • Deficiency of xylulokinase
  • Deficiency, beta ketothiolase
  • Deficiency, holocarboxylase synthease
  • Disorder involving deficiency of steryl-sulfatase
  • Glycerol kinase deficiency - contiguous gene syndrome
  • Hereditary angioedema
  • Hereditary angioneurotic edema
  • Hereditary angioneurotic edema with normal C1 esterase inhibitor activity
  • Holocarboxylase synthase deficiency
  • Holocarboxylase synthetase deficiency
  • Metachromatic leukodystrophy due to deficiency of cerebroside sulfatase activator
  • Muscle AMP deaminase deficiency
  • Muscle L-lactate dehydrogenase deficiency
  • Myoadenylate deaminase deficiency
  • Pancreatic alpha-amylase deficiency
  • Phosphoglycerokinase deficiency
  • Specific enzyme deficiency
  • Succinate-coenzyme Q reductase deficiency
  • Ubiquinone dehydrogenase
Clinical Information
  • Recurring attacks of transient edema suddenly appearing in areas of the skin or mucous membranes and occasionally of the viscera, often associated with dermatographism, urticaria, erythema, and purpura.
Applies To
  • Hereditary angioedema
Convert to ICD-10-CM: 277.6 converts approximately to:
  • 2014 ICD-10-CM D84.1 Defects in the complement system
ICD-9-CM Volume 2 Index entries containing back-references to 277.6:
  • Angioedema (allergic) (any site) (with urticaria) 995.1
    • hereditary 277.6
  • Angioneurotic edema (allergic) (any site) (with urticaria) 995.1
    • hereditary 277.6
  • Deficiency, deficient
    • biotinidase 277.6
    • bradykinase-1 277.6
    • dihydropyrimidine dehydrogenase (DPD) 277.6
    • enzymes, circulating NEC (see also Deficiency, by specific enzyme) 277.6
  • Dihydropyrimidine dehydrogenase disease (DPD) 277.6
  • DPD (dihydropyrimidine dehydrogenase deficiency) 277.6
  • Edema, edematous 782.3
    • angioneurotic (allergic) (any site) (with urticaria) 995.1
      • hereditary 277.6
    • circumscribed, acute 995.1
      • hereditary 277.6
    • essential, acute 995.1
      • hereditary 277.6
    • glottis, glottic, glottides (obstructive) (passive) 478.6
      • allergic 995.1
        • hereditary 277.6
      • due to external agent - see Condition, respiratory, acute, due to specified agent
    • periodic 995.1
      • hereditary 277.6
    • Quincke's 995.1
      • hereditary 277.6
  • Giant
    • urticaria 995.1
      • hereditary 277.6
  • Periodic - see also condition
    • edema 995.1
      • hereditary 277.6
  • Urticaria 708.9
    • with angioneurotic edema 995.1
      • hereditary 277.6
    • giant 995.1
      • hereditary 277.6
    • gigantea 995.1
      • hereditary 277.6
    • larynx 995.1
      • hereditary 277.6
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.6 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.