Specific code 2014 ICD-9-CM Diagnosis Code 277.31
Familial Mediterranean fever
  • Billable Code
  • Short description: Fam Mediterranean fever.
  • ICD-9-CM 277.31 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 277.31 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Familial mediterranean fever
Clinical Information
  • A group of hereditary autoinflammation diseases, characterized by recurrent fever, abdominal pain, headache, rash, pleurisy; and arthritis. Orchitis; benign meningitis; and amyloidosis may also occur. Homozygous or compound heterozygous mutations in marenostrin gene result in autosomal recessive transmission; simple heterozygous, autosomal dominant form of the disease.
  • A usually autosomal recessive inherited inflammatory disorder caused by mutations in the mefv gene. It is characterized by recurrent painful inflammatory attacks in the abdomen, joints, and chest. The inflammatory attacks are associated with fever.
Applies To
  • Benign paroxysmal peritonitis
  • Hereditary amyloid nephropathy
  • Periodic familial polyserositis
  • Recurrent polyserositis
Convert to ICD-10-CM: 277.31 converts approximately to:
  • 2014 ICD-10-CM E85.0 Non-neuropathic heredofamilial amyloidosis
ICD-9-CM Volume 2 Index entries containing back-references to 277.31:
  • Abdominalgia 789.0
    • periodic 277.31
  • Armenian disease 277.31
  • Disease, diseased - see also Syndrome
    • Armenian 277.31
    • familial periodic 277.31
    • periodic (familial) (Reimann's) NEC 277.31
    • Reimann's (periodic) 277.31
    • Siegal-Cattan-Mamou (periodic) 277.31
  • Fever 780.60
    • etiocholanolone 277.31
    • Mediterranean (see also Brucellosis) 023.9
      • familial 277.31
      • tick 082.1
    • periodic 277.31
  • Mediterranean
    • fever (see also Brucellosis) 023.9
      • familial 277.31
  • Nephropathy (see also Nephritis) 583.9
    • hereditary amyloid 277.31
  • Periodic - see also condition
    • disease (familial) 277.31
    • fever 277.31
    • peritonitis 277.31
    • polyserositis 277.31
  • Peritonitis (acute) (adhesive) (fibrinous) (hemorrhagic) (idiopathic) (localized) (perforative) (primary) (with adhesions) (with effusion) 567.9
    • paroxysmal, benign 277.31
    • periodic (familial) 277.31
  • Polyserositis (peritoneal) 568.82
    • paroxysmal (familial) 277.31
    • periodic (familial) 277.31
    • recurrent 277.31
  • Reimann's periodic disease 277.31
  • Siegal-Cattan-Mamou disease (periodic) 277.31
  • Syndrome - see also Disease
    • Armenian 277.31
    • periodic 277.31
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.31 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.