Specific code 2014 ICD-9-CM Diagnosis Code 258.02
Multiple endocrine neoplasia [MEN] type IIA
  • Billable Code
  • Short description: Mult endo neop type IIA.
  • ICD-9-CM 258.02 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 258.02 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Multiple endocrine neoplasia type 2A
  • Multiple endocrine neoplasia type 2A cancerous
  • Multiple endocrine neoplasia type 2A noncancerous
  • Multiple endocrine neoplasia type 2A, benign
  • Multiple endocrine neoplasia type 2A, malignant
  • Multiple endocrine neoplasia, type 2
Clinical Information
  • A form of multiple endocrine neoplasia characterized by the presence of medullary carcinoma (carcinoma, medullary) of the thyroid gland, and usually with the co-occurrence of pheochromocytoma, producing calcitonin and adrenaline, respectively. Less frequently, it can occur with hyperplasia or adenoma of the parathyroid glands. This disease is due to gain-of-function mutations of the men2 gene on chromosome 10 (locus: 10q11.2), also known as the ret proto-oncogene that encodes a receptor protein-tyrosine kinase. It is an autosomal dominant inherited disease.
  • Multiple endocrine neoplasia caused by mutation of the ret gene. Patients develop medullary thyroid carcinomas, and may also develop pheochromocytomas and parathyroid gland hyperplasia.
Applies To
  • Sipple's syndrome
Convert to ICD-10-CM: 258.02 converts directly to:
  • 2014 ICD-10-CM E31.22 Multiple endocrine neoplasia [MEN] type IIA
ICD-9-CM Volume 2 Index entries containing back-references to 258.02:
  • MEN (multiple endocrine neoplasia) syndromes
    • type IIA 258.02
  • Neoplasia
    • multiple endocrine (MEN)
  • Sipple's syndrome (medullary thyroid carcinoma-pheochromocytoma) 258.02
  • Syndrome - see also Disease
    • MEN (multiple endocrine neoplasia)
    • multiple
    • Sipple's (medullary thyroid carcinoma-pheochromocytoma) 258.02
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 258.02 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.