Specific code 2014 ICD-9-CM Diagnosis Code 258.01
Multiple endocrine neoplasia [MEN] type I
  • Billable Code
  • Short description: Mult endo neoplas type I.
  • ICD-9-CM 258.01 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 258.01 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
Disease Synonyms
  • Multiple endocrine neoplasia syndrome
  • Multiple endocrine neoplasia type 1
  • Multiple endocrine neoplasia, type 1
  • Multiple endocrine neoplasm type 1
  • Polyglandular activity in multiple endocrine adenomatosis
Clinical Information
  • A form of multiple endocrine neoplasia that is characterized by the combined occurrence of tumors in the parathyroid glands, the pituitary gland, and the pancreatic islets. The resulting clinical signs include hyperparathyroidism; hypercalcemia; hyperprolactinemia; cushing disease; gastrinoma; and zollinger-ellison syndrome. This disease is due to loss-of-function of the men1 gene, a tumor suppressor gene (genes, tumor suppressor) on chromosome 11 (locus: 11q13).
  • A rare, inherited disorder that affects the endocrine glands and can cause tumors in the parathyroid and pituitary glands and the pancreas. These tumors are usually benign (not cancer). They cause the glands to secrete high levels of hormones, which can lead to other medical problems, such as kidney stones, fertility problems, and severe ulcers. In some cases, tumors inside the pancreas can become malignant (cancer).
  • Multiple endocrine neoplasia caused by inactivation of the tumor suppressor gene men-1. Patients may develop hyperparathyroidism and parathyroid gland adenomas, pituitary gland adenomas, pancreatic islet cell neoplasms, and carcinoid tumors.
Applies To
  • Wermer's syndrome
Convert to ICD-10-CM: 258.01 converts directly to:
  • 2014 ICD-10-CM E31.21 Multiple endocrine neoplasia [MEN] type I
ICD-9-CM Volume 2 Index entries containing back-references to 258.01:
  • Disease, diseased - see also Syndrome
    • Wermer's 258.01
  • MEN (multiple endocrine neoplasia) syndromes
    • type I 258.01
  • Neoplasia
    • multiple endocrine (MEN)
  • Syndrome - see also Disease
    • MEN (multiple endocrine neoplasia)
    • multiple
    • Wermer's (polyendocrine adenomatosis) 258.01
  • Wermer's syndrome or disease (polyendocrine adenomatosis) 258.01
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 258.01 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.