Non-specific code 2014 ICD-9-CM Diagnosis Code 200.3
Marginal zone lymphoma
  • Non-Billable Code
  • There are 9 ICD-9-CM codes below 200.3 that define this diagnosis in greater detail. Do not use this code on a reimbursement claim.
Clinical Information
  • A b-cell non-hodgkin lymphoma composed of small lymphocytes which surround and replace the splenic white pulp germinal centers. It involves the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood. Patients present with splenomegaly and the clinical course is indolent. (who, 2001)
  • A b-cell non-hodgkin lymphoma composed of small lymphocytes which surround and replace the splenic white pulp germinal centers. Neoplastic villous lymphocytes are present in the peripheral blood.
  • A primary nodal b-cell non-hodgkin lymphoma which morphologically resembles lymph nodes involved by marginal zone lymphomas of extranodal or splenic types, but without evidence of extranodal or splenic disease. This is a rare entity, and most patients present with localized or generalized lymphadenopathy. The clinical course is indolent. (who, 2001)
  • A usually indolent mature b-cell lymphoma, arising from the marginal zone of lymphoid tissues. It is characterized by the presence of small to medium sized atypical lymphocytes. It comprises three entities, according to the anatomic sites involved: extranodal marginal zone b-cell lymphoma of mucosa-associated lymphoid tissue, which affects extranodal sites (most often stomach, lung, skin, and ocular adnexa); nodal marginal zone b-cell lymphoma, which affects lymph nodes without evidence of extranodal disease; and splenic marginal zone b-cell lymphoma, which affects the spleen and splenic hilar lymph nodes, bone marrow, and often the peripheral blood.
  • An indolent (slow-growing) type of b-cell non-hodgkin lymphoma that begins forming in certain areas (the marginal zones) of lymph tissue. There are three types based on whether it forms in the spleen, lymph nodes, or other lymphoid tissue that contains a lot of b cells (a type of white blood cell).
  • Lymphoid tissue located beneath the mucosal epithelia of those mucosal surfaces that have contact with the external environment, such as the respiratory, digestive, and urinary systems. Malt consists of a collection of predominantly small lymphocytes, fewer larger, transformed lymphocytes, and plasma cells. It protects the body from pathogens that enter via the mucosa. Malt gives rise to a distinctive type of b-cell lymphoma that usually follows an indolent clinical course.
Applies To
  • Extranodal marginal zone B cell lymphoma
  • Mucosa associated lymphoid tissue [MALT]
  • Nodal marginal zone B cell lymphoma
  • Splenic marginal zone B cell lymphoma
ICD-9-CM Volume 2 Index entries containing back-references to 200.3:
  • Lymphoma (malignant) (M9590/3) 202.8
    • marginal zone 200.3
      • extranodal B-cell 200.3
      • nodal B-cell 200.3
      • splenic B-cell 200.3
  • MALT (mucosa associated lymphoid tissue) 200.3
  • Mucosa associated lymphoid tissue (MALT) 200.3
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 200.3 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2014 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.