2013 ICD-9-CM Diagnosis Code 757.33
Congenital pigmentary anomalies of skin
- most common form of mastocytosis, characterized by multiple persistant small reddish brown hyperpigmented pruritic macules and papules.
- The most frequent form of cutaneous mastocytosis. In children, the lesions tend to be papular, and are characterized by aggregates of elongated or spindle-shaped mast cells which fill the papillary dermis and extend into the reticular dermis. In adults, the lesions tend to have fewer mast cells compared to those in children. The lesions are located most commonly on the trunk, but they can be seen on the extremities, head and neck. (WHO, 2001) -- 2003
- rare pigmentary atrophic autosomal recessive disease manifested as an extreme photosensitivity to ultraviolet light as the result of a deficiency in the enzyme that permits excisional repair of utraviolet damaged DNA.
- A genetic condition characterized by a sensitivity to all sources of ultraviolet radiation.
- An inherited skin disorder characterized by photosensitivity with severe sunburn in infancy, the development of numerous pigmented spots resembling freckles, larger atrophic lesions associated with telangiectasis, and multiple solar keratoses. Transmitted in an autosomal recessive manner, xeroderma pigmentosa involves a defect in nucleotide excision repair (NER), leading to deficient repair of DNA damaged by UV radiation and chromosome breakage. Individuals with this disease develop multiple malignant cutaneous neoplasms at an early age and may suffer from severe ophthalmic and neurologic abnormalities.
- ICD-9-CM 757.33 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
757.33 Excludes 
)Applies To
Convert 757.33 to ICD-10-CM
ICD-9-CM Volume 2 Index entries containing back-references to 757.33:
pigmentosum et atrophicum 
congenital 
