Specific code 2012 ICD-9-CM Diagnosis Code 359.1
Hereditary progressive muscular dystrophy
  • Short description: Hered prog musc dystrphy.
  • ICD-9-CM 359.1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 359.1 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
  • You are viewing the 2012 version of ICD-9-CM 359.1.
  • More recent version(s) of ICD-9-CM 359.1: 2013 2014 2015.
Convert to ICD-10-CM: 359.1 converts directly to:
  • 2015/16 ICD-10-CM G71.0 Muscular dystrophy
Approximate Synonyms
  • Distal muscular dystrophy
  • Duchenne muscular dystrophy
  • Emery Dreifuss muscular dystrophy
  • Emery-Dreifuss muscular dystrophy
  • Erbs muscular dystrophy
  • Erb's muscular dystrophy
  • Facioscapulohumeral muscular dystrophy
  • Kearns-Sayre syndrome (disorder)
  • Limb girdle muscular dystrophy
  • Limb-girdle muscular dystrophy
  • Mitochondrial myopathy, ocular
  • Mitochondrial ocular myopathy
  • Muscular dystrophy
  • Muscular dystrophy, distal
  • Muscular dystrophy, Duchenne
  • Muscular dystrophy, Emery Dreifuss
  • Muscular dystrophy, Erbs
  • Muscular dystrophy, facioscapulohumeral
  • Muscular dystrophy, hereditary progressive
  • Muscular dystrophy, limb girdle
  • Muscular dystrophy, neuropathic
  • Muscular dystrophy, ocular
  • Muscular dystrophy, oculopharyngeal
  • Neuropathic muscular dystrophy
  • Ocular muscular dystrophy
  • Oculopharyngeal muscular dystrophy
  • Restrictive lung disease due to muscular dystrophy
  • Restrictive lung mechanics due to muscular dystrophy
Applies To
  • Muscular dystrophy:
    • NOS
    • distal
    • Duchenne
    • Erb's
    • fascioscapulohumeral
    • Gower's
    • Landouzy-Déjérine
    • limb-girdle
    • ocular
    • oculopharyngeal
ICD-9-CM Volume 2 Index entries containing back-references to 359.1:
  • Atrophy, atrophic
    • facioscapulohumeral (Landouzy-Déjérine) 359.1
    • Landouzy-Déjérine 359.1
    • pseudohypertrophic 359.1
  • Disease, diseased - see also Syndrome
    • Duchenne's 094.0
      • locomotor ataxia 094.0
      • muscular dystrophy 359.1
      • paralysis 335.22
      • pseudohypertrophy, muscles 359.1
    • Duchenne-Griesinger 359.1
    • Erb (-Landouzy) 359.1
  • Disorder - see also Disease
  • Duchenne's
    • disease 094.0
      • locomotor ataxia 094.0
      • muscular dystrophy 359.1
      • pseudohypertrophy, muscles 359.1
  • Duchenne-Griesinger disease 359.1
  • Dystrophy, dystrophia 783.9
    • Duchenne's 359.1
    • Erb's 359.1
    • Gowers' muscular 359.1
    • hereditary, progressive muscular 359.1
    • Landouzy-Déjérine 359.1
    • Leyden-Möbius 359.1
    • muscular 359.1
      • congenital (hereditary) 359.0
      • distal 359.1
      • Duchenne's 359.1
      • Erb's 359.1
      • fascioscapulohumeral 359.1
      • Gowers' 359.1
      • hereditary (progressive) 359.1
      • Landouzy-Déjérine 359.1
      • limb-girdle 359.1
      • myotonic 359.21
      • progressive (hereditary) 359.1
        • Charcôt-Marie-Tooth 356.1
      • pseudohypertrophic (infantile) 359.1
    • ocular 359.1
    • oculopharyngeal 359.1
    • pelvicrural atrophic 359.1
    • progressive ophthalmoplegic 359.1
    • scapuloperoneal 359.1
  • Erb's
    • disease 359.1
    • pseudohypertrophic muscular dystrophy 359.1
  • Facioscapulohumeral myopathy 359.1
  • Gowers'
    • muscular dystrophy 359.1
  • Hypertrophy, hypertrophic
    • pseudomuscular 359.1
  • Landouzy-Déjérine dystrophy (fascioscapulohumeral atrophy) 359.1
  • Leyden-Möbius dystrophy 359.1
  • Myopathy 359.9
    • distal 359.1
    • facioscapulohumeral 359.1
    • limb-girdle 359.1
    • ocular 359.1
    • oculopharyngeal 359.1
    • scapulohumeral 359.1
  • Ocular muscle - see also condition
    • myopathy 359.1
  • Paralysis, paralytic (complete) (incomplete) 344.9
    • muscle (flaccid) 359.9
      • due to nerve lesion NEC 355.9
      • eye (extrinsic) 378.55
      • iris sphincter 364.89
      • ischemic (complicating trauma) (Volkmann's) 958.6
      • pseudohypertrophic 359.1
    • pseudohypertrophic 359.1
      • muscle 359.1
  • Paresis (see also Paralysis) 344.9
    • pseudohypertrophic 359.1
  • Pseudohypertrophic muscular dystrophy (Erb's) 359.1
  • Pseudohypertrophy, muscle 359.1
  • Scapulohumeral myopathy 359.1
  • Syndrome - see also Disease
    • scapuloperoneal 359.1
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 359.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2012 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.