2012 ICD-9-CM Diagnosis Code 277.00
Cystic fibrosis without mention of meconium ileus
- most common potentially lethal autosomal recessive disease affecting Caucasians; characterized by chronic pulmonary, intestinal, liver, pancreatic, and exocrine gland dysfunction; caused by mutations of the CFTR chloride channel.
- A common hereditary disease in which exocrine (secretory) glands produce abnormally thick mucus. This mucus can cause problems in digestion, breathing, and body cooling.
- A congenital metabolic disorder affecting the exocrine glands, inherited as an autosomal trait. The secretions of exocrine glands are abnormal, resulting in excessively viscid mucus production which causes obstruction of passageways (including pancreatic and bile ducts, intestines, and bronchi). The sweat sodium and chloride content are increased. Symptoms usually appear in childhood and include meconium ileus, poor growth despite good appetite, malabsorption and foul bulky stools, chronic bronchitis with cough, recurrent pneumonia, bronchiectasis, emphysema, clubbing of the fingers, and salt depletion in hot weather. -- 2003
- Short description: Cystic fibros w/o ileus.
- ICD-9-CM 277.00 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
- You are viewing the 2012 version of ICD-9-CM 277.00.
- More recent version(s) of ICD-9-CM 277.00: 2013.
Applies To
Convert 277.00 to ICD-10-CM 
ICD-9-CM Volume 2 Index entries containing back-references to 277.00:
due to
bronzed diabetes 
