Specific code 2011 ICD-9-CM Diagnosis Code 330.0
Leukodystrophy
  • ICD-9-CM 330.0 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 330.0 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
  • You are viewing the 2011 version of ICD-9-CM 330.0.
  • More recent version(s) of ICD-9-CM 330.0: 2012 2013 2014.
Disease Synonyms
  • Canavan disease
  • Galactosylceramide beta-galactosidase deficiency
  • Globoid cell leukodystrophy, early onset
  • Globoid cell leukodystrophy, late onset
  • Globoid cell leukodystrophy, late-onset (disorder)
  • Krabbe disease
  • Krabbes disease
  • Metachromatic leucodystrophy (disorder)
  • Metachromatic leukodystrophy
  • Pelizaeus Merzbacher disease
  • Pelizaeus-Merzbacher disease (disorder)
  • Spongy degeneration of central nervous system (disorder)
Applies To
  • Krabbe's disease
  • Leukodystrophy:
    • NOS
    • globoid cell
    • metachromatic
    • sudanophilic
  • Pelizaeus-Merzbacher disease
  • Sulfatide lipidosis
Convert to ICD-10-CM: 330.0 converts approximately to:
  • 2014 ICD-10-CM E75.23 Krabbe disease
    Or:
  • 2014 ICD-10-CM E75.25 Metachromatic leukodystrophy
    Or:
  • 2014 ICD-10-CM E75.29 Other sphingolipidosis
ICD-9-CM Volume 2 Index entries containing back-references to 330.0:
  • Aplasia - see also Agenesis
    • axialis extracorticalis (congenital) 330.0
    • extracortical axial 330.0
    • Pelizaeus-Merzbacher 330.0
  • Canavan's disease 330.0
  • Disease, diseased - see also Syndrome
    • Canavan's 330.0
    • Greenfield's 330.0
    • Krabbe's 330.0
    • Merzbacher-Pelizaeus 330.0
    • Pelizaeus-Merzbacher 330.0
      • with dementia
        • with behavioral disturbance 330.0 [294.11]
        • without behavioral disturbance 330.0 [294.10]
    • Scholz's 330.0
    • van Bogaert-Nijssen (-Peiffer) 330.0
  • Encephalopathy (acute) 348.30
    • leukopolio 330.0
  • Greenfield's disease 330.0
  • Krabbe's
    • disease (leukodystrophy) 330.0
  • Leukodystrophy (cerebral) (globoid cell) (metachromatic) (progressive) (sudanophilic) 330.0
  • Leukoencephalopathy (see also Encephalitis) 323.9
    • metachromatic 330.0
  • Leukopolioencephalopathy 330.0
  • Lipidosis 272.7
    • sulfatide 330.0
  • Merzbacher-Pelizaeus disease 330.0
  • Myeloleukodystrophy 330.0
  • Pelizaeus-Merzbacher
    • disease 330.0
    • sclerosis, diffuse cerebral 330.0
  • Scholz's disease 330.0
  • Scholz (-Bielschowsky-Henneberg) syndrome 330.0
  • Sclerosis, sclerotic
    • brain (general) (lobular) 348.89
      • Alzheimer's - see Alzheimer's, dementia
      • artery, arterial 437.0
      • atrophic lobar 331.0
      • diffuse 341.1
        • familial (chronic) (infantile) 330.0
        • infantile (chronic) (familial) 330.0
        • Pelizaeus-Merzbacher type 330.0
      • disseminated 340
      • hereditary 334.2
      • hippocampal 348.81
      • infantile (degenerative) (diffuse) 330.0
      • insular 340
      • Krabbe's 330.0
      • mesial temporal 348.81
      • miliary 340
      • multiple 340
      • Pelizaeus-Merzbacher 330.0
      • progressive familial 330.0
      • senile 437.0
      • temporal 348.81
      • tuberous 759.5
    • centrolobar, familial 330.0
  • Sulfatidosis 330.0
  • Syndrome - see also Disease
    • Scholz (-Bielschowsky-Henneberg) 330.0
  • van Bogaert-Nijssen (-Peiffer) disease 330.0
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 330.0 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2011 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.