Specific code 2010 ICD-9-CM Diagnosis Code 416.0
Primary pulmonary hypertension
  • Short description: Prim pulm hypertension.
  • ICD-9-CM 416.0 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 416.0 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
  • You are viewing the 2010 version of ICD-9-CM 416.0.
  • More recent version(s) of ICD-9-CM 416.0: 2011 2012 2013 2014 2015.
Convert to ICD-10-CM: 416.0 converts directly to:
  • 2015/16 ICD-10-CM I27.0 Primary pulmonary hypertension
Approximate Synonyms
  • Primary pulmonary HTN
  • PRIMARY PULMONARY HYPERTENSION
  • Pulmonary HTN, primary
Applies To
  • Idiopathic pulmonary arteriosclerosis
  • Pulmonary hypertension (essential) (idiopathic) (primary)
ICD-9-CM Volume 2 Index entries containing back-references to 416.0:
  • Arrillaga-Ayerza syndrome (pulmonary artery sclerosis with pulmonary hypertension) 416.0
  • Arteriosclerosis, arteriosclerotic (artery) (deformans) (diffuse) (disease) (endarteritis) (general) (obliterans) (obliterative) (occlusive) (senile) (with calcification) 440.9
    • pulmonary (idiopathic) 416.0
  • Ayerza's disease or syndrome (pulmonary artery sclerosis with pulmonary hypertension) 416.0
  • Cardiopathia nigra 416.0
  • Disease, diseased - see also Syndrome
    • Ayerza's (pulmonary artery sclerosis with pulmonary hypertension) 416.0
    • heart (organic) 429.9
      • with
        • acute pulmonary edema (see also Failure, ventricular, left) 428.1
          • hypertensive 402.91
          • kidney disease - see Hypertension, cardiorenal
          • rheumatic fever (conditions classifiable to 390)
      • amyloid 277.39[425.7]
      • aortic (valve) (see also Endocarditis, aortic) 424.1
      • arteriosclerotic or sclerotic (minimal) (senile) - see Arteriosclerosis, coronary
      • artery, arterial - see Arteriosclerosis, coronary
      • atherosclerotic - see Arteriosclerosis, coronary
      • beer drinkers' 425.5
      • beriberi 265.0 [425.7]
      • black 416.0
      • congenital NEC 746.9
        • cyanotic 746.9
        • maternal, affecting fetus or newborn 760.3
        • specified type NEC 746.89
      • congestive (see also Failure, heart) 428.0
      • coronary 414.9
      • cryptogenic 429.9
      • due to
      • fetal 746.9
      • fibroid (see also Myocarditis) 429.0
      • functional 427.9
      • glycogen storage 271.0 [425.7]
      • gonococcal NEC 098.85
      • gouty 274.82
      • hypertensive (see also Hypertension, heart) 402.90
      • hyperthyroid (see also Hyperthyroidism) 242.9 [425.7]
      • incompletely diagnosed - see Disease, heart
      • ischemic (chronic) (see also Ischemia, heart) 414.9
        • acute (see also Infarct, myocardium) 410.9
          • without myocardial infarction 411.89
            • with coronary (artery) occlusion 411.81
        • asymptomatic 412
        • diagnosed on ECG or other special investigation but currently presenting no symptoms 412
      • kyphoscoliotic 416.1
      • mitral (see also Endocarditis, mitral) 394.9
      • muscular (see also Degeneration, myocardial) 429.1
      • postpartum 674.8
      • psychogenic (functional) 306.2
      • pulmonary (chronic) 416.9
      • rheumatic (chronic) (inactive) (old) (quiescent) (with chorea) 398.90
        • active or acute 391.9
          • with chorea (active) (rheumatic) (Sydenham's) 392.0
          • specified type NEC 391.8
        • maternal, affecting fetus or newborn 760.3
      • rheumatoid - see Arthritis, rheumatoid
      • sclerotic - see Arteriosclerosis, coronary
      • senile (see also Myocarditis) 429.0
      • specified type NEC 429.89
      • syphilitic 093.89
      • thyroid (gland) (see also Hyperthyroidism) 242.9 [425.7]
      • thyrotoxic (see also Thyrotoxicosis) 242.9 [425.7]
      • tuberculous (see also Tuberculosis) 017.9 [425.8]
      • valve, valvular (obstructive) (regurgitant) - see also Endocarditis
        • congenital NEC (see also Anomaly, heart, valve) 746.9
      • vascular - see Disease, cardiovascular
    • pulmonary - see also Disease, lung
      • amyloid 277.39 [517.8]
      • artery 417.9
      • circulation, circulatory 417.9
      • diffuse obstructive (chronic) 496
        • with
          • acute bronchitis 491.22
          • asthma (chronic) (obstructive) 493.2
          • exacerbation NEC (acute) 491.21
      • heart (chronic) 416.9
      • hypertensive (vascular) 416.0
        • cardiovascular 416.0
      • obstructive diffuse (chronic) 496
      • valve (see also Endocarditis, pulmonary) 424.3
  • Sclerosis, sclerotic
    • pulmonary (see also Fibrosis, lung) 515
      • artery 416.0
      • valve (heart) (see also Endocarditis, pulmonary) 424.3
  • Syndrome - see also Disease
    • Arrillaga-Ayerza (pulmonary artery sclerosis with pulmonary hypertension) 416.0
    • Ayerza (-Arrillaga) (pulmonary artery sclerosis with pulmonary hypertension) 416.0
    • cardiacos negros 416.0
    • pulmonary
      • arteriosclerosis 416.0
      • hypoperfusion (idiopathic) 769
      • renal (hemorrhagic) 446.21
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 416.0 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2010 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.