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2009 ICD-9-CM Diagnosis Code 046
Slow virus infection and prion diseases of central nervous system
2009 ICD-9-CM Diagnosis Code 046.1
Jakob-creutzfeldt disease
2009 ICD-9-CM Diagnosis Code 046.11
Variant creutzfeldt-jakob disease
2009 ICD-9-CM Diagnosis Code 046.19
Other and unspecified creutzfeldt-jakob disease
2009 ICD-9-CM Diagnosis Code 046.2
Subacute sclerosing panencephalitis
  • rare chronic progressive encephalitis caused by the measles virus and occurring primarily in children and young adults; death usually occurs within three years; characterized by primary measles infection before the age of two years.
2009 ICD-9-CM Diagnosis Code 046.3
Progressive multifocal leukoencephalopathy
  • demyelination in various part of the central nervous system, usually secondary to neoplastic disease; JC virus has been recovered from brain tissue.
2009 ICD-9-CM Diagnosis Code 046.7
Other specified prion diseases of central nervous system
2009 ICD-9-CM Diagnosis Code 046.71
Gerstmann-straussler-scheinker syndrome
2009 ICD-9-CM Diagnosis Code 046.79
Other and unspecified prion disease of central nervous system
2009 ICD-9-CM Diagnosis Code 046.8
Other specified slow virus infection of central nervous system
2009 ICD-9-CM Diagnosis Code 046.9
Unspecified slow virus infection of central nervous system