2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Congential Anomalies 740-759 > Other And Unspecified Congenital Anomalies 759.* > 2008 ICD-9-CM Diagnosis 759.81 Prader-willi syndrome  On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date. The 2009 version of ICD-9-CM 759.81 can be accessed here. A chromosomal disorder associated with a deletion of the proximal portion of the long arm of chromosome 15 (15q11-q13) in the majority of affected individuals. The abnormalities occur exclusively on the paternally derived chromosome 15. Clinical manifestations include MENTAL RETARDATION, muscular hypotonia, OBESITY, hyperphagia, short stature, hypogonadism, strabismus, and hypersomnolence. (Menkes, Textbook of Child Neurology, 5th ed, p229) A syndrome characterized at birth by the lack of spontaneous movements and protective reflexes, thus giving an appearance of severe brain damage. Profound hypotonia may cause asphyxia. Sucking and swallowing reflexes are absent or decreased. Deficient thermoregulation, amyotonia, and hypogonadism are usually associated. After a few weeks or months, the affected infants become more responsive and more alert. Areflexia disappears gradually but hypotonia may persist longer. This phase is marked mainly by mental subnormality, delayed growth and motor development, speech defect, lack of emotional control, voracious appetite leading to obesity, hypotonia, hyperlaxity, delayed bone maturation, and multiple orofacial and other disoders. There is a tendency to develop diabetes mellitus and cardiac failure in some patients. Pain insensitivity is common. Prader-Willi habitus associated with osteopenia and camptodactyly is known as the Urban-Rogers-Meyer syndrome. 759.81 is a specific code that can be used to specify a diagnosis 759.81 contains 9 index entries View the ICD-9-CM Volume 1 759.* hierarchy ICD9Data's sister site ProcedureCodes.com launches with the 2008/09 CPT® codes - read more on the ICD9Data.com blog. Index entries containing 759.81: Dystrophy, dystrophia 783.9 hypogenital, with diabetic tendency 759.81 Prader-Labhart-Willi-Fanconi syndrome (hypogenital dystrophy with diabetic tendency) 759.81 Prader-Willi syndrome (hypogenital dystrophy with diabetic tendency) 759.81 Syndrome - see also Disease H3O 759.81 HHHO 759.81 hypotonia-hypomentia-hypogonadism-obesity 759.81 Prader (-Labhart)-Willi (-Fanconi) 759.81 Willi-Prader (hypogenital dystrophy with diabetic tendency) 759.81 Willi-Prader syndrome (hypogenital dystrophy with diabetic tendency) 759.81