2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Congential Anomalies 740-759 >
 Congenital anomalies of the integument- Congenital structural abnormalities of the skin.
- 757 is a non-specific code that cannot be used to specify a diagnosis
Hereditary edema of legs- 757.0 is a specific code that can be used to specify a diagnosis
- 757.0 contains 23 index entries
Ichthyosis congenita- Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
- 757.1 is a specific code that can be used to specify a diagnosis
- 757.1 contains 25 index entries
Dermatoglyphic anomalies- 757.2 is a specific code that can be used to specify a diagnosis
- 757.2 contains 3 index entries
Other specified congenital anomalies of skin- 757.3 is a non-specific code that cannot be used to specify a diagnosis
Congenital ectodermal dysplasia- A group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. They are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. They are generally nonprogressive and diffuse. Various forms exist, including anhidrotic and hidrotic dysplasias, FOCAL DERMAL HYPOPLASIA, and aplasia cutis congenita.
- 757.31 is a specific code that can be used to specify a diagnosis
- 757.31 contains 13 index entries
Vascular hamartomas- A dull red, firm, dome-shaped hemangioma, sharply demarcated from surrounding skin, usually located on the head and neck, which grows rapidly and generally undergoes regression and involution without scarring. It is caused by proliferation of immature capillary vessels in active stroma, and is usually present at birth or occurs within the first two or three months of life. (Dorland, 27th ed)
- A vascular malformation of developmental origin characterized pathologically by ectasia of superficial dermal capillaries, and clinically by persistent macular erythema. In the past, port wine stains have frequently been termed capillary hemangiomas, which they are not; unfortunately this confusing practice persists: HEMANGIOMA, CAPILLARY is neoplastic, a port-wine stain is non-neoplastic. Port-wine stains vary in color from fairly pale pink to deep red or purple and in size from a few millimeters to many centimeters in diameter. The face is the most frequently affected site and they are most often unilateral. (From Rook et al., Textbook of Dermatology, 5th ed, p483)
- 757.32 is a specific code that can be used to specify a diagnosis
- 757.32 contains 16 index entries
Congenital pigmentary anomalies of skin- A genetic condition characterized by a sensitivity to all sources of ultraviolet radiation.
- A rare, pigmentary, and atrophic autosomal recessive disease affecting all races. It is manifested as an extreme photosensitivity to ultraviolet light as the result of a deficiency in the enzyme that permits excisional repair of ultraviolet-damaged DNA.
- An autosomal recessive syndrome occurring principally in females, characterized by the presence of reticulated, atrophic, hyperpigmented, telangiectatic cutaneous plaques, often accompanied by juvenile cataracts, saddle nose, congenital bone defects, disturbances in the growth of hair, nails, and teeth, and hypogonadism.
- An inherited skin disorder characterized by photosensitivity with severe sunburn in infancy, the development of numerous pigmented spots resembling freckles, larger atrophic lesions associated with telangiectasis, and multiple solar keratoses. Transmitted in an autosomal recessive manner, xeroderma pigmentosa involves a defect in nucleotide excision repair (NER), leading to deficient repair of DNA damaged by UV radiation and chromosome breakage. Individuals with this disease develop multiple malignant cutaneous neoplasms at an early age and may suffer from severe ophthalmic and neurologic abnormalities. --2004
- The most common form of cutaneous mastocytosis (MASTOCYTOSIS, CUTANEOUS) that occurs primarily in children. It is characterized by the multiple small reddish-brown pigmented pruritic macules and papules.
- The most frequent form of cutaneous mastocytosis. In children, the lesions tend to be papular, and are characterized by aggregates of elongated or spindle-shaped mast cells which fill the papillary dermis and extend into the reticular dermis. In adults, the lesions tend to have fewer mast cells compared to those in children. The lesions are located most commonly on the trunk, but they can be seen on the extremities, head and neck. (WHO, 2001) -- 2003
- 757.33 is a specific code that can be used to specify a diagnosis
- 757.33 contains 48 index entries
Other specified congenital anomalies of skin- Group of genetically determined disorders characterized by the blistering of skin and mucosae. There are four major forms: acquired, simple, junctional, and dystrophic. Each of the latter three has several varieties.
- 757.39 is a specific code that can be used to specify a diagnosis
- 757.39 contains 119 index entries
Specified congenital anomalies of hair- 757.4 is a specific code that can be used to specify a diagnosis
- 757.4 contains 32 index entries
Specified congenital anomalies of nails- 757.5 is a specific code that can be used to specify a diagnosis
- 757.5 contains 40 index entries
Specified congenital anomalies of breast- 757.6 is a specific code that can be used to specify a diagnosis
- 757.6 contains 27 index entries
Other specified congenital anomalies of the integument- 757.8 is a specific code that can be used to specify a diagnosis
- 757.8 contains 4 index entries
Unspecified congenital anomaly of the integument- Congenital structural abnormalities of the skin.
- 757.9 is a specific code that can be used to specify a diagnosis
- 757.9 contains 17 index entries
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