2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Congential Anomalies 740-759 > Other Congenital Anomalies Of Heart 746.* > 2008 ICD-9-CM Diagnosis 746.01 Atresia of pulmonary valve congenital  On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date. The 2009 version of ICD-9-CM 746.01 can be accessed here. Congenital absence of the normal valvular orifice into the pulmonary artery. This condition is characterized by cardiomegaly, reduced pulmonary vascularity, and right ventricular atrophy. (From Stedman, 25th ed; Dorland, 27th ed) 746.01 is a specific code that can be used to specify a diagnosis 746.01 contains 10 index entries View the ICD-9-CM Volume 1 746.* hierarchy ICD9Data's sister site ProcedureCodes.com launches with the 2008/09 CPT® codes - read more on the ICD9Data.com blog. 746.01 also known as: Congenital absence of pulmonary valve Index entries containing 746.01: Absence (organ or part) (complete or partial) pulmonary valve (congenital) 746.01 Agenesis - see also Absence, by site, congenital heart 746.89 valve NEC 746.89 pulmonary 746.01 Anomaly, anomalous (congenital) (unspecified type) 759.9 heart 746.9 valve NEC 746.9 pulmonary 746.00 atresia 746.01 pulmonary 748.60 valve 746.00 atresia 746.01 Atresia, atretic (congenital) 759.89 cardiac valve 746.89 pulmonary 746.01 heart valve NEC 746.89 pulmonary 746.01 pulmonary (artery) 747.3 valve 746.01 pulmonic 746.01 Hypoplasia, hypoplasis 759.89 heart 746.89 valve NEC 746.89 pulmonary 746.01 pulmonary 748.5 valve 746.01