2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Hereditary And Degenerative Diseases Of The Central Nervous System 330-337 >
 Other extrapyramidal disease and abnormal movement disorders- 333 is a non-specific code that cannot be used to specify a diagnosis
Other degenerative diseases of the basal ganglia- A degenerative disease of the central nervous system characterized by balance difficulties; OCULAR MOTILITY DISORDERS (supranuclear ophthalmoplegia); DYSARTHRIA; swallowing difficulties; and axial DYSTONIA. Onset is usually in the fifth decade and disease progression occurs over several years. Pathologic findings include neurofibrillary degeneration and neuronal loss in the dorsal MESENCEPHALON; SUBTHALAMIC NUCLEUS; RED NUCLEUS; pallidum; dentate nucleus; and vestibular nuclei. (From Adams et al., Principles of Neurology, 6th ed, pp1076-7)
- A group of inherited and sporadic disorders which share progressive ataxia in combination with atrophy of the CEREBELLUM; PONS; and inferior olivary nuclei. Additional clinical features may include MUSCLE RIGIDITY; NYSTAGMUS; RETINAL DEGENERATION; MUSCLE SPASTICITY; DEMENTIA; URINARY INCONTINENCE; and OPHTHALMOPLEGIA. The familial form has an earlier onset (second decade) and may feature spinal cord atrophy. The sporadic form tends to present in the fifth or sixth decade, and is considered a clinical subtype of MULTIPLE SYSTEM ATROPHY. (From Adams et al., Principles of Neurology, 6th ed, p1085)
- A progressive neurodegenerative condition of the central and autonomic nervous systems characterized by atrophy of the preganglionic lateral horn neurons of the thoracic spinal cord, which differentiates this condition from other forms of idiopathic orthostatic hypotension (HYPOTENSION, ORTHOSTATIC). This disease is generally considered a clinical variant of MULTIPLE SYSTEM ATROPHY. Affected individuals present in the fifth or sixth decade with orthostasis and bladder dysfunction; and later develop FECAL INCONTINENCE; anhidrosis; ATAXIA; IMPOTENCE; and alterations of tone suggestive of basal ganglia dysfunction. (From Adams et al., Principles of Neurology, 6th ed, p536)
- A rare autosomal recessive degenerative disorder which usually presents in late childhood or adolescence. Clinical manifestations include progressive MUSCLE SPASTICITY; hyperreflexia; MUSCLE RIGIDITY; DYSTONIA; DYSARTHRIA; and intellectual deterioration which progresses to severe dementia over several years. Pathologic examination reveals neuronal atrophy in the globus pallidus and iron deposition in blood vessels and perivascular spaces. (From Adams et al., Principles of Neurology, 6th ed, p972; Davis & Robertson, Textbook of Neuropathology, 2nd ed, pp972-929)
- A rare neuroaxonal dystrophy, histologically characterized by axonal spheroids, iron deposition, lewy body (LB)-like intraneuronal inclusions and neurofibrillary tangles.
- 333.0 is a specific code that can be used to specify a diagnosis
- 333.0 contains 24 index entries
Essential and other specified forms of tremor- A relatively common disorder characterized by a fairly specific pattern of tremors which are most prominent in the upper extremities and neck, inducing titubations of the head. The tremor is usually mild, but when severe may be disabling. An autosomal dominant pattern of inheritance may occur in some families (i.e., familial tremor). (Mov Disord 1988;13(1):5-10)
- 333.1 is a specific code that can be used to specify a diagnosis
- 333.1 contains 7 index entries
Myoclonus- A heterogeneous group of primarily familial disorders characterized by myoclonic seizures, tonic-clonic seizures, ataxia, progressive intellectual deterioration, and neuronal degeneration. These include LAFORA DISEASE; MERRF SYNDROME; NEURONAL CEROID-LIPOFUSCINOSIS; sialidosis (see MUCOLIPIDOSES), and UNVERRICHT-LUNDBORG SYNDROME.
- An autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ATAXIA, slowly progressive intellectual deterioration, dysarthria, and intention tremor. Myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. The age of onset is between 8 and 13 years, and the condition is relatively frequent in the Baltic region, especially Finland. (From Menkes, Textbook of Child Neurology, 5th ed, pp109-110)
- Involuntary shock-like contractions, irregular in rhythm and amplitude, followed by relaxation, of a muscle or a group of muscles. This condition may be a feature of some CENTRAL NERVOUS SYSTEMS DISEASES (e.g., EPILEPSY, MYOCLONIC). Nocturnal myoclonus may represent a normal physiologic event or occur as the principal feature of the NOCTURNAL MYOCLONUS SYNDROME. (From Adams et al., Principles of Neurology, 6th ed, pp102-3).
- 333.2 is a specific code that can be used to specify a diagnosis
- 333.2 contains 22 index entries
Tics of organic origin- 333.3 is a specific code that can be used to specify a diagnosis
- 333.3 contains 2 index entries
Huntington's chorea- A familial disorder inherited as an autosomal dominant trait and characterized by the onset of progressive CHOREA and DEMENTIA in the fourth or fifth decade of life. Common initial manifestations include paranoia; poor impulse control; DEPRESSION; HALLUCINATIONS; and DELUSIONS. Eventually intellectual impairment; loss of fine motor control; ATHETOSIS; and diffuse chorea involving axial and limb musculature develops, leading to a vegetative state within 10-15 years of disease onset. The juvenile variant has a more fulminant course including SEIZURES; ATAXIA; dementia; and chorea. (From Adams et al., Principles of Neurology, 6th ed, pp1060-4)
- KEGG_ID: hsa05040
- 333.4 is a specific code that can be used to specify a diagnosis
- 333.4 contains 9 index entries
Other choreas- 333.5 is a specific code that can be used to specify a diagnosis
- 333.5 contains 6 index entries
Idiopathic torsion dystonia- A condition characterized by focal DYSTONIA that progresses to involuntary spasmodic contractions of the muscles of the legs, trunk, arms, and face. The hands are often spared, however, sustained axial and limb contractions may lead to a state where the body is grossly contorted. Onset is usually in the first or second decade. Familial patterns of inheritance, primarily autosomal dominant with incomplete penetrance, have been identified. (Adams et al., Principles of Neurology, 6th ed, p1078)
- 333.6 is a specific code that can be used to specify a diagnosis
- 333.6 contains 12 index entries
Symptomatic torsion dystonia- 333.7 is a non-specific code that cannot be used to specify a diagnosis
- 333.7 contains 1 index entry
Athetoid cerebral palsy- 333.71 is a specific code that can be used to specify a diagnosis
- 333.71 contains 6 index entries
Acute dystonia due to drugs- 333.72 is a specific code that can be used to specify a diagnosis
- 333.72 contains 3 index entries
Other acquired torsion dystonia- 333.79 is a specific code that can be used to specify a diagnosis
- 333.79 contains 4 index entries
Fragments of torsion dystonia- 333.8 is a non-specific code that cannot be used to specify a diagnosis
Blepharospasm- Excessive winking; tonic or clonic spasm of the orbicularis oculi muscle.
- 333.81 is a specific code that can be used to specify a diagnosis
- 333.81 contains 3 index entries
Orofacial dyskinesia- 333.82 is a specific code that can be used to specify a diagnosis
- 333.82 contains 3 index entries
Spasmodic torticollis- A twisted neck symptom that is caused by the spasmodic involuntary muscle contractions in the neck region.
- 333.83 is a specific code that can be used to specify a diagnosis
- 333.83 contains 1 index entry
Organic writers' cramp- 333.84 is a specific code that can be used to specify a diagnosis
- 333.84 contains 8 index entries
Subacute dyskinesia due to drugs- 333.85 is a specific code that can be used to specify a diagnosis
- 333.85 contains 5 index entries
Other fragments of torsion dystonia- 333.89 is a specific code that can be used to specify a diagnosis
- 333.89 contains 3 index entries
Other and unspecified extrapyramidal diseases and abnormal movement disorders- 333.9 is a non-specific code that cannot be used to specify a diagnosis
Unspecified extrapyramidal disease and abnormal movement disorder- 333.90 is a specific code that can be used to specify a diagnosis
- 333.90 contains 12 index entries
Stiff-man syndrome- A condition characterized by persistent spasms (SPASM) involving multiple muscles, primarily in the lower limbs and trunk. The illness tends to occur in the fourth to sixth decade of life, presenting with intermittent spasms that become continuous. Minor sensory stimuli, such as noise and light touch, precipitate severe spasms. Spasms do not occur during sleep and only rarely involve cranial muscles. Respiration may become impaired in advanced cases. (Adams et al., Principles of Neurology, 6th ed, p1492; Neurology 1998 Jul;51(1):85-93)
- 333.91 is a specific code that can be used to specify a diagnosis
- 333.91 contains 2 index entries
Neuroleptic malignant syndrome- A potentially fatal syndrome associated primarily with the use of neuroleptic agents (see ANTIPSYCHOTIC AGENTS) which are in turn associated with dopaminergic receptor blockade (see RECEPTORS, DOPAMINE) in the BASAL GANGLIA and HYPOTHALAMUS, and sympathetic dysregulation. Clinical features include diffuse MUSCLE RIGIDITY; TREMOR; high FEVER; diaphoresis; labile blood pressure; cognitive dysfunction; and autonomic disturbances. Serum CPK level elevation and a leukocytosis may also be present. (From Adams et al., Principles of Neurology, 6th ed, p1199; Psychiatr Serv 1998 Sep;49(9):1163-72)
- 333.92 is a specific code that can be used to specify a diagnosis
- 333.92 contains 2 index entries
Benign shuddering attacks- 333.93 is a specific code that can be used to specify a diagnosis
- 333.93 contains 1 index entry
Restless legs syndrome- 333.94 is a specific code that can be used to specify a diagnosis
- 333.94 contains 4 index entries
Other extrapyramidal diseases and abnormal movement disorders- A disorder characterized by aching or burning sensations in the lower and rarely the upper extremities that occur prior to sleep or may awaken the patient from sleep. Complying with an irresistible urge to move the affected limbs brings temporary relief. Sleep may become disrupted, resulting in excessive daytime hypersomnolence. This condition may be associated with UREMIA; DIABETES; and rheumatoid arthritis. Restless Legs Syndrome differs from NOCTURNAL MYOCLONUS SYNDROME in that in the latter condition the individual does not report adverse sensory stimuli and it is primarily a sleep-associated movement disorder. (Adams et al., Principles of Neurology, 6th ed, p387; Schweiz Rundsch Med Prax 1997 Apr 30;86(18):732-736)
- 333.99 is a specific code that can be used to specify a diagnosis
- 333.99 contains 8 index entries
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