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2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Other Metabolic Disorders And Immunity Disorders 270-279 > Other And Unspecified Disorders Of Metabolism 277.* > 2008 ICD-9-CM Diagnosis 277.4 Disorders of bilirubin excretion  On October 1, 2008 the 2009 ICD-9-CM codes came into effect. Therefore, this code may be out of date. The 2009 version of ICD-9-CM 277.4 can be accessed here. A benign familial disorder, transmitted as an autosomal dominant trait. It is characterized by low-grade chronic hyperbilirubinemia with considerable daily fluctuations of the bilirubin level. A benign, autosomally recessive inherited hyperbilirubinemia characterized by the presence of a dark pigment in the centrilobular region of the liver cells. There is a functional defect in biliary excretion of bilirubin, cholephilic dyes, and porphyrins. Affected persons may be asymptomatic or have vague constitutional or gastrointestinal symptoms. The liver may be slightly enlarged, and oral and intravenous cholangiography fails to visualize the biliary tract. A familial form of congenital hyperbilirubinemia transmitted as an autosomal recessive trait. It is characterized by icterus and brain damage caused by a glucuronyl transferase deficiency in the liver and faulty bilirubin conjugation. 277.4 is a specific code that can be used to specify a diagnosis 277.4 contains 28 index entries View the ICD-9-CM Volume 1 277.* hierarchy 277.4 also known as: Hyperbilirubinemia: congenital constitutional Syndrome: Crigler-Najjar Dubin-Johnson Gilbert's Rotor's 277.4 excludes: hyperbilirubinemias specific to the perinatal period (774.0-774.7) Index entries containing 277.4: Cholemia (see also Jaundice) 782.4 familial 277.4 Gilbert's (familial nonhemolytic) 277.4 Crigler-Najjar disease or syndrome (congenital hyperbilirubinemia) 277.4 Defect, defective 759.9 bilirubin excretion 277.4 Deficiency, deficient glucuronyl transferase 277.4 Disease, diseased - see also Syndrome Crigler-Najjar (congenital hyperbilirubinemia) 277.4 Gilbert's (familial nonhemolytic jaundice) 277.4 Disorder - see also Disease bilirubin excretion 277.4 metabolism NEC 277.9 bilirubin 277.4 Dubin-Johnson disease or syndrome 277.4 Dysfunction liver 573.9 constitutional 277.4 Findings, abnormal, without diagnosis (examination) (laboratory test) 796.4 bilirubin 277.4 Gilbert's disease or cholemia (familial nonhemolytic jaundice) 277.4 Hyperbilirubinemia 782.4 congenital 277.4 constitutional 277.4 Icterus (see also Jaundice) 782.4 intermittens juvenilis 277.4 Jaundice (yellow) 782.4 chronic idiopathic 277.4 Gilbert's (familial nonhemolytic) 277.4 idiopathic, chronic 277.4 nonhemolytic, congenital familial (Gilbert's) 277.4 Rotor's disease or syndrome (idiopathic hyperbilirubinemia) 277.4 Syndrome - see also Disease Crigler-Najjar (congenital hyperbilirubinemia) 277.4 Dubin-Johnson (constitutional hyperbilirubinemia) 277.4 Dubin-Sprinz (constitutional hyperbilirubinemia) 277.4 Gilbert's 277.4 glucuronyl transferase 277.4 Rotor's (idiopathic hyperbilirubinemia) 277.4 Thesaurismosis bilirubin 277.4