A rare aggressive form of lymphoma (cancer that begins in cells of the lymphatic system) that is usually of T-cell origin.
A peripheral (mature) T-cell lymphoma, consisting of usually large anaplastic, CD30 positive cells. The majority of cases are positive for the anaplastic large cell lymphoma (ALK) protein. The most frequently seen genetic alteration is a t(2;5) translocation. Majority of patients present with advanced disease. The most important prognostic indicator is ALK positivity, which has been associated with a favorable prognosis. (WHO, 2001)
ICD-9-CM Volume 2 Index Entries That Refer To 200.6