Specific code 2008 ICD-9-CM Diagnosis Code 046.1
Jakob-creutzfeldt disease
  • Short description: JAKOB-CREUTZFELDT DIS.
  • ICD-9-CM 046.1 is a billable medical code that can be used to indicate a diagnosis on a reimbursement claim, however, 046.1 should only be used for claims with a date of service on or before September 30, 2015. For claims with a date of service on or after October 1, 2015, use an equivalent ICD-10-CM code (or codes).
  • You are viewing the 2008 version of ICD-9-CM 046.1.
  • More recent version(s) of ICD-9-CM 046.1: 2009 2010 2011 2012 2013 2014 2015.
  • No ICD-10-CM code(s) convert to ICD-9-CM 046.1
Applies To
  • Subacute spongiform encephalopathy
ICD-9-CM Volume 2 Index entries containing back-references to 046.1:
  • Creutzfeldt-Jakob disease (syndrome) (new variant) 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]
  • Disease, diseased - see also Syndrome
    • Creutzfeldt-Jakob (new variant) 046.1
      • with dementia
        • with behavioral disturbance 046.1 [294.11]
        • without behavioral disturbance 046.1 [294.10]
    • Jakob-Creutzfeldt (new variant) 046.1
      • with dementia
        • with behavioral disturbance 046.1 [294.11]
        • without behavioral disturbance 046.1 [294.10]
  • Encephalopathy (acute) 348.30
    • spongioform, subacute (viral) 046.1
    • subacute
      • necrotizing 330.8
      • spongioform 046.1
      • viral, spongioform 046.1
  • Jakob-Creutzfeldt disease (syndrome) (new variant) 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]
  • Pseudosclerosis (brain)
    • Jakob's 046.1
    • spastic 046.1
      • with dementia
        • with behavioral disturbance 046.1 [294.11]
        • without behavioral disturbance 046.1 [294.10]
  • Syndrome - see also Disease
    • Creutzfeldt-Jakob (new variant) 046.1
      • with dementia
        • with behavioral disturbance 046.1 [294.11]
        • without behavioral disturbance 046.1 [294.10]
    • Jakob-Creutzfeldt (new variant) 046.1
      • with dementia
        • with behavioral disturbance 046.1 [294.11]
        • without behavioral disturbance 046.1 [294.10]
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 046.1 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2008 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.