ICD9Data.com
  Free 2008 ICD-9-CM Database
Search ICD9Data.com

2008 ICD-9-CM Volume 1 Diagnosis Codes Home > Infectious And Parasitic Diseases 001-139 > Poliomyelitis And Other Non-Arthropod-Borne Viral Diseases Of Central Nervous System 045-049 > Slow Virus Infection Of Central Nervous System 046.* >

2008 ICD-9-CM Diagnosis 046.1

Jakob-creutzfeldt disease

  • A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances, personality changes, ATAXIA; APHASIA, visual loss, weakness, muscle atrophy, MYOCLONUS, progressive dementia, and death within one year of disease onset. A familial form exhibiting autosomal dominant inheritance and a new variant CJD (potentially associated with ENCEPHALOPATHY, BOVINE SPONGIFORM) have been described. Pathological features include prominent cerebellar and cerebral cortical spongiform degeneration and the presence of PRIONS. (From N Engl J Med, 1998 Dec 31;339(27))
  • 046.1 is a specific code that can be used to specify a diagnosis
  • 046.1 contains 11 index entries
  • View the ICD-9-CM Volume 1 046.* hierarchy

046.1 also known as:

  • Subacute spongiform encephalopathy


Index entries containing 046.1:

Creutzfeldt-Jakob disease (syndrome) (new variant) 046.1
  • with dementia
    • with behavioral disturbance 046.1 [294.11]
    • without behavioral disturbance 046.1 [294.10]
Disease, diseased - see also Syndrome
  • Creutzfeldt-Jakob (new variant) 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]
  • Jakob-Creutzfeldt (new variant) 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]
Encephalopathy (acute) 348.30
  • spongioform, subacute (viral) 046.1
  • subacute
    • spongioform 046.1
    • viral, spongioform 046.1
Jakob-Creutzfeldt disease (syndrome) (new variant) 046.1
  • with dementia
    • with behavioral disturbance 046.1 [294.11]
    • without behavioral disturbance 046.1 [294.10]
Pseudosclerosis (brain)
  • Jakob's 046.1
  • spastic 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]
Syndrome - see also Disease
  • Creutzfeldt-Jakob (new variant) 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]
  • Jakob-Creutzfeldt (new variant) 046.1
    • with dementia
      • with behavioral disturbance 046.1 [294.11]
      • without behavioral disturbance 046.1 [294.10]