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2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Other Metabolic Disorders And Immunity Disorders 270-279 > Other And Unspecified Disorders Of Metabolism 277.* >

2007 ICD-9-CM Diagnosis 277.89

Other specified disorders of metabolism

This code may be outdated. View the most recent version of ICD-9-CM 277.89

  • A neoplastic proliferation of Langerhans cells which contain Birbeck granules by ultrastructural examination. Three major overlapping syndromes are recognized: eosinophilic granuloma, Letterer-Siwe disease, and Hand-Schuller-Christian disease. The clinical course is generally related to the number of organs affected at presentation. (WHO, 2001) -- 2003
  • Disseminated, chronic form of Langerhans-cell histiocytosis. It may exhibit the classic triad of exophthalmos, diabetes insipidus, and bone destruction.
  • General term for the abnormal appearance of histiocytes in the blood. Based on the pathological features of the cells involved rather than on clinical findings, the histiocytic diseases are subdivided into three groups: HISTIOCYTOSIS, LANGERHANS CELL; HISTIOCYTOSIS, NON-LANGERHANS CELL; and HISTIOCYTIC DISORDERS, MALIGNANT.
  • Group of disorders of histiocyte proliferation which includes LETTERER-SIWE DISEASE; HAND-SCHUELLER-CHRISTIAN SYNDROME; and EOSINOPHILIC GRANULOMA. Langerhans cells are components of the lesions.
  • 277.89 is a specific code that can be used to specify a diagnosis
  • 277.89 contains 29 index entries
  • View the ICD-9-CM Volume 1 277.* hierarchy

277.89 also known as:

  • Hand-Schüller-Christian disease
  • Histiocytosis (acute) (chronic)
  • Histiocytosis X (chronic)

277.89 excludes:

  • histiocytosis:
    • acute differentiated progressive (202.5)
    • X, acute (progressive) (202.5)

Index entries containing 277.89:

Acatalasemia 277.89
Acatalasia 277.89
Christian's syndrome (chronic histiocytosis X) 277.89
Disease, diseased - see also Syndrome
  • Christian's (chronic histiocytosis X) 277.89
  • Hand-Schüller-Christian (chronic histiocytosis X) 277.89
  • Schüller-Christian (chronic histiocytosis X) 277.89
Disorder - see also Disease
  • metabolism NEC 277.9
    • specified type NEC 277.89
Eosinophilic - see also condition
  • granuloma (bone) 277.89
Granuloma NEC 686.1
  • bone (see also Osteomyelitis) 730.1
    • eosinophilic 277.89
  • eosinophilic 277.89
    • bone 277.89
    • lung 277.89
    • oral mucosa 528.9
  • lipid 277.89
  • lipoid 277.89
  • lung (infectious) (see also Fibrosis, lung) 515
    • eosinophilic 277.89
  • reticulohistiocytic 277.89
Granulomatosis NEC 686.1
  • lipoid 277.89
Hand-Schüller-Christian disease or syndrome (chronic histiocytosis x) 277.89
Histiocytosis (acute) (chronic) (subacute) 277.89
  • acute differentiated progressive (M9722/3) 202.5
  • cholesterol 277.89
  • essential 277.89
  • lipid, lipoid (essential) 272.7
  • lipochrome (familial) 288.1
  • malignant (M9720/3) 202.3
  • X (chronic) 277.89
    • acute (progressive) (M9722/3) 202.5
Metabolism disorder 277.9
  • specified type NEC 277.89
Reticulohistiocytoma (giant cell) 277.89
Schüller-Christian disease or syndrome (chronic histiocytosis X) 277.89
Syndrome - see also Disease
  • Christian's (chronic histiocytosis X) 277.89
  • Hand-Schüller-Christian (chronic histiocytosis X) 277.89
  • Schüller-Christian (chronic histiocytosis X) 277.89
Xanthoma(s), xanthomatosis 272.2
  • craniohypophyseal 277.89