Specific code 2007 ICD-9-CM Diagnosis Code 277.5
Mucopolysaccharidosis
  • ICD-9-CM 277.5 will be replaced by an equivalent ICD-10-CM code (or codes) when the United States transitions from ICD-9-CM to ICD-10-CM on October 1, 2015.
  • ICD-9-CM 277.5 is a billable medical code that can be used to specify a diagnosis on a reimbursement claim.
  • You are viewing the 2007 version of ICD-9-CM 277.5.
  • More recent version(s) of ICD-9-CM 277.5: 2008 2009 2010 2011 2012 2013 2014.
Disease Synonyms
  • Disorder of glycosaminoglycan metabolism
  • Glucosaminoglycan metabolism disorder
  • Maroteaux Lamy syndrome
  • Maroteaux-Lamy syndrome
  • Morquio syndrome
  • Mucopolysaccharidosis 2
  • Mucopolysaccharidosis MPS-I-H
  • Mucopolysaccharidosis MPS-I-H/S
  • Mucopolysaccharidosis MPS-II
  • Mucopolysaccharidosis MPS-I-S
  • Mucopolysaccharidosis MPS-IV-A
  • Mucopolysaccharidosis MPS-IV-B
  • Mucopolysaccharidosis type IVB (disorder)
  • Mucopolysaccharidosis, MPS-I-H
  • Mucopolysaccharidosis, MPS-I-H/S
  • Mucopolysaccharidosis, MPS-II
  • Mucopolysaccharidosis, MPS-I-S
  • Mucopolysaccharidosis, MPS-IV-A
  • Mucopolysaccharidosis, MPS-IV-B
  • Sanfilippo syndrome
Applies To
  • Gargoylism
  • Hunter's syndrome
  • Hurler's syndrome
  • Lipochondrodystrophy
  • Maroteaux-Lamy syndrome
  • Morquio-Brailsford disease
  • Osteochondrodystrophy
  • Sanfilippo's syndrome
  • Scheie's syndrome
Convert to ICD-10-CM: 277.5 converts approximately to:
  • 2014 ICD-10-CM E76.01 Hurler's syndrome
    Or:
  • 2014 ICD-10-CM E76.03 Scheie's syndrome
    Or:
  • 2014 ICD-10-CM E76.1 Mucopolysaccharidosis, type II
    Or:
  • 2014 ICD-10-CM E76.219 Morquio mucopolysaccharidoses, unspecified
    Or:
  • 2014 ICD-10-CM E76.22 Sanfilippo mucopolysaccharidoses
    Or:
  • 2014 ICD-10-CM E76.29 Other mucopolysaccharidoses
    Or:
  • 2014 ICD-10-CM E76.3 Mucopolysaccharidosis, unspecified
ICD-9-CM Volume 2 Index entries containing back-references to 277.5:
  • Brailsford-Morquio disease or syndrome (mucopolysaccharidosis IV) 277.5
  • Chondrodystrophia (fetalis) 756.4
    • tarda 277.5
  • Chondro-osteodysplasia (Morquio-Brailsford type) 277.5
  • Chondro-osteodystrophy 277.5
  • Disease, diseased - see also Syndrome
    • Brailsford-Morquio (mucopolysaccharidosis IV) 277.5
    • Hurler's (mucopolysaccharidosis I) 277.5
    • Morquio (-Brailsford) (-Ullrich) (mucopolysaccharidosis IV) 277.5
    • storage
      • glycogen (see also Disease, glycogen storage) 271.0
      • lipid 272.7
      • mucopolysaccharide 277.5
  • Disorder - see also Disease
    • mucopolysaccharide 277.5
  • Dwarf, dwarfism 259.4
    • polydystrophic 277.5
  • Dysostosis
    • multiplex 277.5
  • Dystrophy, dystrophia 783.9
    • familial
      • hyperplastic periosteal 756.59
      • osseous 277.5
  • Eccentro-osteochondrodysplasia 277.5
  • Gargoylism 277.5
  • Heparitinuria 277.5
  • Hunter (-Hurler) syndrome (mucopolysaccharidosis II) 277.5
  • Hurler (-Hunter) disease or syndrome (mucopolysaccharidosis II) 277.5
  • Lipochondrodystrophy 277.5
  • Maroteaux-Lamy syndrome (mucopolysaccharidosis VI) 277.5
  • Morquio (-Brailsford) (-Ullrich) disease or syndrome (mucopolysaccharidosis IV) 277.5
    • kyphosis 277.5
  • Mucopolysaccharidosis (types 1-6) 277.5
    • cardiopathy 277.5 [425.7]
  • Osteochondrodystrophy 277.5
    • deformans 277.5
    • familial 277.5
  • Polydystrophic oligophrenia 277.5
  • Sanfilippo's syndrome (mucopolysaccharidosis III) 277.5
  • Scheie's syndrome (mucopolysaccharidosis IS) 277.5
  • Syndrome - see also Disease
    • Brailsford-Morquio (dystrophy) (mucopolysaccharidosis IV) 277.5
    • Hunter (-Hurler) (mucopolysaccharidosis II) 277.5
    • Hurler (-Hunter) (mucopolysaccharidosis II) 277.5
    • Maroteaux-Lamy (mucopolysaccharidosis VI) 277.5
    • Morquio (-Brailsford) (-Ullrich) (mucopolysaccharidosis IV) 277.5
    • Sanfilippo's (mucopolysaccharidosis III) 277.5
    • Scheie's (mucopolysaccharidosis IS) 277.5
ICD-9-CM codes are used in medical billing and coding to describe diseases, injuries, symptoms and conditions. ICD-9-CM 277.5 is one of thousands of ICD-9-CM codes used in healthcare. Although ICD-9-CM and CPT codes are largely numeric, they differ in that CPT codes describe medical procedures and services. Can't find a code? Start at the root of ICD-9-CM, check the 2007 ICD-9-CM Index or use the search engine at the top of this page to lookup any code.