2007 ICD-9-CM Volume 1 Diagnosis Codes Home > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Other Metabolic Disorders And Immunity Disorders 270-279 > Other And Unspecified Disorders Of Metabolism 277.* >
 2007 ICD-9-CM Diagnosis 277.00
Cystic fibrosis without meconium ileusThis code may be outdated. View the most recent version of ICD-9-CM 277.00 - A common hereditary disease in which exocrine (secretory) glands produce abnormally thick mucus. This mucus can cause problems in digestion, breathing, and body cooling.
- A congenital metabolic disorder affecting the exocrine glands, inherited as an autosomal trait. The secretions of exocrine glands are abnormal, resulting in excessively viscid mucus production which causes obstruction of passageways (including pancreatic and bile ducts, intestines, and bronchi). The sweat sodium and chloride content are increased. Symptoms usually appear in childhood and include meconium ileus, poor growth despite good appetite, malabsorption and foul bulky stools, chronic bronchitis with cough, recurrent pneumonia, bronchiectasis, emphysema, clubbing of the fingers, and salt depletion in hot weather. -- 2003
- An autosomal recessive genetic disease of the EXOCRINE GLANDS. It is caused by mutations in the gene encoding the CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR expressed in several organs including the LUNG, the PANCREAS, the BILIARY SYSTEM, and the SWEAT GLANDS. Cystic fibrosis is characterized by epithelial secretory dysfunction associated with ductal obstruction resulting in AIRWAY OBSTRUCTION; chronic RESPIRATORY INFECTIONS; PANCREATIC INSUFFICIENCY; maldigestion; salt depletion; and HEAT PROSTRATION.
- 277.00 is a specific code that can be used to specify a diagnosis
- 277.00 contains 9 index entries
- View the ICD-9-CM Volume 1 277.* hierarchy
277.00 also known as:
Index entries containing 277.00:- Cirrhosis, cirrhotic 571.5
- due to
- cystic fibrosis
 277.00
Cystic - see also condition- fibrosis (pancreas) 277.00
- with
- manifestations
- meconium ileus 277.01
- pulmonary exacerbation 277.02
Disease, diseased - see also Syndrome- pancreas 577.9
- fibrocystic 277.00
Fibrocystic- disease 277.00
Fibrosis, fibrotic- cystic (of pancreas) 277.00
- with
- manifestations
- meconium ileus 277.01
- pulmonary exacerbation 277.02
- pancreas 577.8
- cystic 277.00
- with
- manifestations
- meconium ileus 277.01
- pulmonary exacerbation 277.02
Hyperviscidosis 277.00
Mucoviscidosis 277.00- with meconium obstruction 277.01
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