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2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > Congenital Anomalies Of The Integument 757.* >

2006 ICD-9-CM Diagnosis 757.1

Ichthyosis congenita

View the most recent version of ICD-9-CM 757.1

  • Designation for several severe forms of ichthyosis, present at birth, that are characterized by hyperkeratotic scaling. Infants may be born encased in a collodion membrane which begins shedding within 24 hours. This is followed in about two weeks by persistent generalized scaling. The forms include bullous (HYPERKERATOSIS, EPIDERMOLYTIC), non-bullous (ICHTHYOSIS, LAMELLAR), wet type, and dry type.
  • 757.1 is a specific code that can be used to specify a diagnosis
  • 757.1 contains 25 index entries
  • View the ICD-9-CM Volume 1 757.* hierarchy

Alternate Terminology

  • Congenital ichthyosis
  • Harlequin fetus
  • Ichthyosiform erythroderma


 Index entries containing 757.1:

Alligator skin disease (ichthyosis congenita) 757.1Carini's syndrome (ichthyosis congenita) 757.1
    Collodion baby (ichthyosis congenita) 757.1
      Disease, diseased - see also Syndrome
      • alligator skin (ichthyosis congenita) 757.1
      • fish skin 757.1
      Erythema, erythematous (generalized) 695.9
      • ichthyosiforme congenitum 757.1
        Erythroderma (see also Erythema) 695.9
        • ichthyosiform, congenital 757.1
          Harlequin (fetus) 757.1Hyperkeratosis (see also Keratosis) 701.1
          • universalis congenita 757.1
            Ichthyosis (congenita) 757.1
            • acquired 701.1
              • fetalis gravior 757.1
                • follicularis 757.1
                  • hystrix 757.39
                    • lamellar 757.1
                      • lingual 528.6
                        • palmaris and plantaris 757.39
                          • simplex 757.1
                            • vera 757.1
                              • vulgaris 757.1
                                Keratoma 701.1
                                • malignum congenitale 757.1
                                  Netherton's syndrome (ichthyosiform erythroderma) 757.1
                                    Seeligmann's syndrome (ichthyosis congenita) 757.1
                                      Sjögren-Larsson syndrome (ichthyosis congenita) 757.1
                                        Syndrome - see also Disease
                                        • Alligator baby (ichthyosis congenita) 757.1
                                          • Carini's (ichthyosis congenita) 757.1
                                            • Netherton's (ichthyosiform erythroderma) 757.1
                                              • Seeligmann's (ichthyosis congenita) 757.1
                                                • Sjögren-Larsson (ichthyosis congenita) 757.1