2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Congenital Anomalies 740-759 > ICD-9-CM Diagnosis 753 Congenital anomalies of urinary system 753 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 753.0 Renal agenesis and dysgenesis 753.0 is a specific code that can be used to specify a diagnosis 753.0 contains 15 index entries ICD-9-CM Diagnosis 753.1 Cystic kidney disease 753.1 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 753.10 Cystic kidney disease unspecified 753.10 is a specific code that can be used to specify a diagnosis 753.10 contains 10 index entries ICD-9-CM Diagnosis 753.11 Congenital single renal cyst Abnormal fluid filled sac within the kidney, either acquired or congenital. 753.11 is a specific code that can be used to specify a diagnosis 753.11 contains 5 index entries ICD-9-CM Diagnosis 753.12 Polycystic kidney unspecified type Diseases that are characterized by the progressive expansion of a large number of tightly packed cysts within the kidney. 753.12 is a specific code that can be used to specify a diagnosis 753.12 contains 7 index entries ICD-9-CM Diagnosis 753.13 Polycystic kidney autosomal dominant A genetic disorder with autosomal dominant inheritance characterized by multiple cysts in both kidneys and progressive deterioration of renal function. Type 1 is usually caused by a mutant gene at the PKD1 locus on the short arm of chromosome 16, though mutations elsewhere in the genome can also cause the disease. The age of onset of symptoms varies widely. 753.13 is a specific code that can be used to specify a diagnosis 753.13 contains 14 index entries ICD-9-CM Diagnosis 753.14 Polycystic kidney autosomal recessive A rare genetic disorder with autosomal recessive inheritance characterized by multiple cysts in both kidneys and associated hepatic lesions. Serious manifestations are usually present at birth and there is high perinatal mortality. 753.14 is a specific code that can be used to specify a diagnosis 753.14 contains 21 index entries ICD-9-CM Diagnosis 753.15 Renal dysplasia 753.15 is a specific code that can be used to specify a diagnosis 753.15 contains 2 index entries ICD-9-CM Diagnosis 753.16 Medullary cystic kidney 753.16 is a specific code that can be used to specify a diagnosis 753.16 contains 4 index entries ICD-9-CM Diagnosis 753.17 Medullary sponge kidney Cystic disease of the medullary portion of the renal pyramids; asymptomatic unless complicated by infection, calculi, or obstruction; should be distinguished from congenital polycystic disease of the kidneys. 753.17 is a specific code that can be used to specify a diagnosis 753.17 contains 2 index entries ICD-9-CM Diagnosis 753.19 Other specified cystic kidney disease A severe form of dysplasia where the kidney typically appears as a bunch of grapes without a reniform configuration or calyceal drainage system. It occurs in-utero and is the most common form of nongenetic renal cystic disease. 753.19 is a specific code that can be used to specify a diagnosis 753.19 contains 15 index entries ICD-9-CM Diagnosis 753.2 Obstructive defects of renal pelvis and ureter 753.2 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 753.20 Unspecified obstructive defect of renal pelvis and ureter 753.20 is a specific code that can be used to specify a diagnosis 753.20 contains 6 index entries ICD-9-CM Diagnosis 753.21 Congenital obstruction of ureteropelvic junction 753.21 is a specific code that can be used to specify a diagnosis 753.21 contains 4 index entries ICD-9-CM Diagnosis 753.22 Congenital obstruction of ureterovesical junction 753.22 is a specific code that can be used to specify a diagnosis 753.22 contains 8 index entries ICD-9-CM Diagnosis 753.23 Congenital ureterocele 753.23 is a specific code that can be used to specify a diagnosis 753.23 contains 1 index entry ICD-9-CM Diagnosis 753.29 Other obstructive defect of renal pelvis and ureter 753.29 is a specific code that can be used to specify a diagnosis 753.29 contains 15 index entries ICD-9-CM Diagnosis 753.3 Other specified anomalies of kidney 753.3 is a specific code that can be used to specify a diagnosis 753.3 contains 63 index entries ICD-9-CM Diagnosis 753.4 Other specified anomalies of ureter 753.4 is a specific code that can be used to specify a diagnosis 753.4 contains 22 index entries ICD-9-CM Diagnosis 753.5 Exstrophy of urinary bladder Congenital eversion of the urinary bladder. It is characterized by the absence of a portion of the lower abdominal wall and the anterior vesical wall, with eversion of the posterior vesical wall through the deficit. 753.5 is a specific code that can be used to specify a diagnosis 753.5 contains 5 index entries ICD-9-CM Diagnosis 753.6 Congenital atresia and stenosis of urethra and bladder neck 753.6 is a specific code that can be used to specify a diagnosis 753.6 contains 25 index entries ICD-9-CM Diagnosis 753.7 Congenital anomalies of urachus Cyst occurring in a persistent portion of the urachus, presenting as an extraperitoneal mass in the umbilical region. It is characterized by abdominal pain, and fever if infected. It may rupture, leading to peritonitis, or it may drain through the umbilicus. 753.7 is a specific code that can be used to specify a diagnosis 753.7 contains 16 index entries ICD-9-CM Diagnosis 753.8 Other specified congenital anomalies of bladder and urethra 753.8 is a specific code that can be used to specify a diagnosis 753.8 contains 49 index entries ICD-9-CM Diagnosis 753.9 Unspecified congenital anomaly of urinary system 753.9 is a specific code that can be used to specify a diagnosis 753.9 contains 18 index entries