2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Circulatory System 390-459 > Diseases Of Arteries, Arterioles, And Capillaries 440-448 > ICD-9-CM Diagnosis 446 Polyarteritis nodosa and allied conditions 446 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 446.0 Polyarteritis nodosa A form of necrotizing vasculitis involving small- and medium-sized arteries. The signs and symptoms result from infarction and scarring of the affected organ system. 446.0 is a specific code that can be used to specify a diagnosis 446.0 contains 14 index entries ICD-9-CM Diagnosis 446.1 Acute febrile mucocutaneous lymph node syndrome (mcls) An acute, febrile, mucocutaneous condition accompanied by swelling of cervical lymph nodes in infants and young children. The principal symptoms are fever, congestion of the ocular conjunctivae, reddening of the lips and oral cavity, protuberance of tongue papillae, and edema or erythema of the extremities. 446.1 is a specific code that can be used to specify a diagnosis 446.1 contains 5 index entries ICD-9-CM Diagnosis 446.2 Hypersensitivity angiitis Heterogeneous group of disorders characterized by a vasculitic syndrome presumed to be associated with a hypersensitivity reaction following exposure to an antigen such as an infectious agent, a drug, or other foreign or endogenous substance (Wilson et al, Harrison's Principles of Internal Medicine, 12th ed, p1459). 446.2 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 446.20 Hypersensitivity angiitis unspecified Heterogeneous group of disorders characterized by a vasculitic syndrome presumed to be associated with a hypersensitivity reaction following exposure to an antigen such as an infectious agent, a drug, or other foreign or endogenous substance (Wilson et al, Harrison's Principles of Internal Medicine, 12th ed, p1459). 446.20 is a specific code that can be used to specify a diagnosis 446.20 contains 5 index entries ICD-9-CM Diagnosis 446.21 Goodpasture's syndrome A combination of pulmonary hemorrhage and glomerulonephritis. It is known also as the lung purpura glomerulonephritis complex. It is considered by some to be a form of hypersensitivity reaction. 446.21 is a specific code that can be used to specify a diagnosis 446.21 contains 6 index entries ICD-9-CM Diagnosis 446.29 Other specified hypersensitivity angiitis 446.29 is a specific code that can be used to specify a diagnosis 446.29 contains 4 index entries ICD-9-CM Diagnosis 446.3 Lethal midline granuloma A non-neoplastic disease of unknown etiology beginning with inflammation, ulceration, and perforation of nose and palate and progressing to gradual destruction of midline facial structures. 446.3 is a specific code that can be used to specify a diagnosis 446.3 contains 6 index entries ICD-9-CM Diagnosis 446.4 Wegener's granulomatosis A multisystem disease chiefly affecting males, characterized by necrotizing granulomatous vasculitis involving the upper and lower respiratory tracts, glomerulonephritis, and variable degrees of systemic, small vessel vasculitis, which is generally considered to represent an aberrant hypersensitivity reaction to an unknown antigen. 446.4 is a specific code that can be used to specify a diagnosis 446.4 contains 11 index entries ICD-9-CM Diagnosis 446.5 Giant cell arteritis A systemic autoimmune vasculitis occurring primarily in people over the age of 50. Pathologic features include a necrotizing panarteritis including granulomas and giant cells. There is a predilection for involvement of central nervous system blood vessels and the most frequent neurologic complication is an OPTIC NEUROPATHY, ISCHEMIC. Large blood vessels may become involved, including the aorta. Clinical manifestations may include myalgias, weight loss, headache, visual loss, necrosis of the skin or tongue, and chest discomfort. Superficial scalp arteries may become tender and enlarged. A related condition, juvenile temporal arteritis, tends to occur in the first or second decade of life. 446.5 is a specific code that can be used to specify a diagnosis 446.5 contains 11 index entries ICD-9-CM Diagnosis 446.6 Thrombotic microangiopathy A disease characterized by thrombocytopenia, hemolytic anemia, bizarre neurological manifestations, azotemia, fever, and thromboses in terminal arterioles and capillaries. 446.6 is a specific code that can be used to specify a diagnosis 446.6 contains 16 index entries ICD-9-CM Diagnosis 446.7 Takayasu's disease A thrombo-obliterative process of the great vessels stemming from the aortic arch, occurring generally in young women. Radial and carotid pulses are typically obliterated. Skin changes are due to the disturbed circulation. There may be loss of hair and atrophy of the skin and its appendages with underlying muscle atrophy. 446.7 is a specific code that can be used to specify a diagnosis 446.7 contains 22 index entries