2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Circulatory System 390-459 > Cerebrovascular Disease 430-438 > Other And Ill-Defined Cerebrovascular Disease 437.* > 2006 ICD-9-CM Diagnosis 437.5 Moyamoya disease View the most recent version of ICD-9-CM 437.5 A chronic cerebral vasculopathy primarily occurring in childhood and characterized by slowly progressive carotid artery narrowing and occlusion at the base of the brain. An extensive network of anastomoses forms between branches of the carotid arteries, resulting in a characteristic angiographic appearance. The condition may be idiopathic (classic moyamoya disease) or occur in association with ANEMIA, SICKLE CELL; DOWN SYNDROME; CRANIOCEREBRAL TRAUMA; RADIOTHERAPY induced arterial injury; NEUROFIBROMATOSIS; and other diseases. Clinical manifestations include hemiparesis, headache, seizures, and delayed mental development. In older individuals, this disease may present as SUBARACHNOID HEMORRHAGE. 437.5 is a specific code that can be used to specify a diagnosis 437.5 contains 4 index entries View the ICD-9-CM Volume 1 437.* hierarchy  Index entries containing 437.5: Disease, diseased - see also Syndrome Moyamoya 437.5 Nishimoto (-Takeuchi) 437.5 Moya Moya disease 437.5 Nishimoto (-Takeuchi) disease 437.5