2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Diseases Of The Nervous System And Sense Organs 320-389 > Disorders Of The Peripheral Nervous System 350-359 > Muscular Dystrophies And Other Myopathies 359.* > 2006 ICD-9-CM Diagnosis 359.2 Myotonic disorders View the most recent version of ICD-9-CM 359.2 An autosomal dominant neuromuscular disorder which usually presents in early adulthood, characterized by progressive muscular atrophy (most frequently involving the hands, forearms, and face), myotonia, frontal baldness, lenticular opacities, and testicular atrophy. Cardiac conduction abnormalities, diaphragmatic weakness, and mild mental retardation may also occur. Congenital myotonic dystrophy is a severe form of this disorder, characterized by neonatal MUSCLE HYPOTONIA, feeding difficulties, respiratory muscle weakness, and an increased incidence of MENTAL RETARDATION. A dominantly inherited muscle disease that begins in early childhood and is characterized by severe myotonia (delayed relaxation of a muscle) after forceful voluntary contractions. Muscular hypertrophy is common and myotonia may impair ambulation and other movements. Myotonia typically becomes less severe with repetitive voluntary contractions of the affected muscles. Generalized myotonia (of Becker) is an autosomal recessive variant of myotonia congenita that may feature more severe myotonia and muscle wasting. Diseases characterized by MYOTONIA, which may be inherited or acquired. Myotonia may be restricted to certain muscles (e.g., intrinsic hand muscles) or occur as a generalized condition. These disorders may be associated with abnormal muscle SODIUM CHANNEL and CHLORIDE CHANNELS. MYOTONIC DYSTROPHY and MYOTONIA CONGENITA represent two relatively common forms of this disorder. Proximal myotonic myopathy often presents with myotonia and muscle pain in early adulthood and later in life thigh muscle weakness and cataracts develop. 359.2 is a specific code that can be used to specify a diagnosis 359.2 contains 26 index entries View the ICD-9-CM Volume 1 359.* hierarchy Alternate Terminology Dystrophia myotonica Eulenburg's disease Myotonia congenita Paramyotonia congenita Steinert's disease Thomsen's disease  Index entries containing 359.2: Atrophy, atrophic muscle, muscular 728.2 myotonic 359.2 myotonia 359.2 Batten-Steinert syndrome 359.2 Curschmann (-Batten) (-Steinert) disease or syndrome 359.2 Disease, diseased - see also Syndrome Batten-Steinert 359.2 Curschmann's 359.2 Eulenburg's (congenital paramyotonia) 359.2 Steinert's 359.2 Thomsen's 359.2 von Eulenburg's (congenital paramyotonia) 359.2 Disorder - see also Disease myotonic 359.2 Dystrophy, dystrophia 783.9 muscular 359.1 congenital (hereditary) 359.0 myotonic 359.2 myotonic 359.2 myotonic 359.2 myotonica 359.2 Eulenburg's disease (congenital paramyotonia) 359.2 Myotonia (acquisita) (intermittens) 728.85 atrophica 359.2 congenita 359.2 dystrophica 359.2 Paramyotonia 359.2 congenita 359.2 Steinert's disease 359.2 Syndrome - see also Disease Batten-Steinert 359.2 Curschmann (-Batten) (-Steinert) 359.2 Thomsen's disease 359.2 von Eulenburg's disease (congenital paramyotonia) 359.2