2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Endocrine, Nutritional And Metabolic Diseases, And Immunity Disorders 240-279 > Diseases Of Other Endocrine Glands 250-259 > Testicular Dysfunction 257.* > 2006 ICD-9-CM Diagnosis 257.8 Other testicular dysfunction View the most recent version of ICD-9-CM 257.8 A disorder also known as complete androgen insensitivity syndrome (CAIS). The 46,XY genetic male totally lacks androgen responsiveness in the target organs thus exhibits a female phenotype. Sexual ambiguity in males due to a sexual differentiation disorder caused by testicular failure to respond to androgens. The affected males have abdominal and inguinal testes, female external genitalia and breasts, blind vaginas, and absent uteri. Some patients have absent pubic and axillary hair, hence the synonym "hairless pseudofemale." Mental retardation occurs in some cases. 257.8 is a specific code that can be used to specify a diagnosis 257.8 contains 3 index entries View the ICD-9-CM Volume 1 257.* hierarchy 257.8 Excludes androgen insensitivity syndrome (259.5)  Index entries containing 257.8: Dysfunction testicular 257.9 specified type NEC 257.8 Syndrome - see also Disease hairless women 257.8 testis, nonvirilizing 257.8