2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Neoplasms 140-239 > Neoplasms Of Uncertain Behavior 235-238 > Neoplasm Of Uncertain Behavior Of Other And Unspecified Sites And Tissues 238.* > 2006 ICD-9-CM Diagnosis 238.4 Polycythemia vera View the most recent version of ICD-9-CM 238.4 A chronic myeloproliferative disorder characterized by an increased red blood cell production. Excessive proliferation of the myeloid lineage is observed as well. The major symptoms are related to hypertension or to vascular abnormalities caused by the increased red cell mass. The cause is unknown. With currently available treatment, the median survival exceeds 10 years. (WHO, 2001) -- 2003 A myeloproliferative disorder of unknown etiology, characterized by abnormal proliferation of all hematopoietic bone marrow elements and an absolute increase in red cell mass and total blood volume, associated frequently with splenomegaly, leukocytosis, and thrombocythemia. Hematopoiesis is also reactive in extramedullary sites (liver and spleen). In time myelofibrosis occurs. 238.4 is a specific code that can be used to specify a diagnosis 238.4 contains 7 index entries View the ICD-9-CM Volume 1 238.* hierarchy  Index entries containing 238.4: Disease, diseased - see also Syndrome Osler (-Vaquez) (polycythemia vera) (M9950/1) 238.4 Vaquez (-Osler) (polycythemia vera) (M9950/1) 238.4 Osler's disease (M9950/1) (polycythemia vera) 238.4 Osler-Vaquez disease (M9950/1) (polycythemia vera) 238.4 Polycythemia (primary) (rubra) (vera) (M9950/1) 238.4 acquired 289.0 benign 289.0 familial 289.6 due to donor twin 776.4 fall in plasma volume 289.0 high altitude 289.0 maternal-fetal transfusion 776.4 stress 289.0 emotional 289.0 erythropoietin 289.0 familial (benign) 289.6 Gaisböck's (hypertonica) 289.0 high altitude 289.0 hypertonica 289.0 hypoxemic 289.0 neonatorum 776.4 nephrogenous 289.0 relative 289.0 secondary 289.0 spurious 289.0 stress 289.0 Vaquez's disease (M9950/1) 238.4 Vaquez-Osler disease (polycythemia vera) (M9950/1) 238.4