2006 ICD-9-CM Volume 1 Diagnosis Codes Home > Neoplasms 140-239 > Neoplasms Of Uncertain Behavior 235-238 > ICD-9-CM Diagnosis 237 Neoplasm of uncertain behavior of endocrine glands and nervous system 237 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 237.0 Neoplasm of uncertain behavior of pituitary gland and craniopharyngeal duct 237.0 is a specific code that can be used to specify a diagnosis 237.0 contains 3 index entries ICD-9-CM Diagnosis 237.1 Neoplasm of uncertain behavior of pineal gland 237.1 is a specific code that can be used to specify a diagnosis 237.1 contains 2 index entries ICD-9-CM Diagnosis 237.2 Neoplasm of uncertain behavior of adrenal gland 237.2 is a specific code that can be used to specify a diagnosis 237.2 contains 1 index entry ICD-9-CM Diagnosis 237.3 Neoplasm of uncertain behavior of paraganglia 237.3 is a specific code that can be used to specify a diagnosis 237.3 contains 12 index entries ICD-9-CM Diagnosis 237.4 Neoplasm of uncertain behavior of other and unspecified endocrine glands 237.4 is a specific code that can be used to specify a diagnosis 237.4 contains 6 index entries ICD-9-CM Diagnosis 237.5 Neoplasm of uncertain behavior of brain and spinal cord 237.5 is a specific code that can be used to specify a diagnosis 237.5 contains 6 index entries ICD-9-CM Diagnosis 237.6 Neoplasm of uncertain behavior of meninges 237.6 is a specific code that can be used to specify a diagnosis 237.6 contains 3 index entries ICD-9-CM Diagnosis 237.7 Neurofibromatosis except of bone NF1. A rare genetic condition that causes brown spots and tumors on the skin, freckling in skin areas not exposed to the sun, tumors on the nerves, and developmental changes in the nervous system, muscles, bone, and skin. Type 1 (peripheral) neurofibromatosis (von Recklinghausen's disease), is the most common type of neurofibromatosis. It is characterized clinically by cutaneous and subcutaneous tumors with patches of hyperpigmentation. The hyperpigmented skin areas, are present from birth and found anywhere on the body surface. They can vary markedly in size and color. The dark brown areas are called cafe-au-lait spots. The multiple cutaneous and subcutaneous tumors are nerve sheath neoplasms, called neurofibromas. They can develop anywhere along the peripheral nerve fibers. Neurofibromas can become quite large, causing a major disfigurement, eroding bone, and compressing various peripheral nerve structures. Type 1 neurofibromatosis has dominant inheritance, with a gene locus on the proximal long arm of chromosome 17. -- 2003 A group of disorders characterized by an autosomal dominant pattern of inheritance with high rates of spontaneous mutation and multiple neurofibromas or neurilemmomas. NEUROFIBROMATOSIS 1 (generalized neurofibromatosis) accounts for approximately 95% of cases, although multiple additional subtypes (e.g., NEUROFIBROMATOSIS 2, neurofibromatosis 3, etc.) have been described. (From Neurochirurgie 1998 Nov;44 An autosomal dominant inherited disorder (with a high frequency of spontaneous mutations) that features developmental changes in the nervous system, muscles, bones, and skin, most notably in tissue derived from the embryonic NEURAL CREST. Multiple hyperpigmented skin lesions and subcutaneous tumors are the hallmark of this disease. Peripheral and central nervous system neoplasms occur frequently, especially OPTIC NERVE GLIOMA and NEUROFIBROSARCOMA. NF1 is caused by mutations which inactivate the NF1 gene (GENES, NEUROFIBROMATOSIS 1) on chromosome 17q. The incidence of learning disabilities is also elevated in this condition. (From Adams et al., Principles of Neurology, 6th ed, pp1014-18) There is overlap of clinical features with NOONAN SYNDROME in a syndrome called neurofibromatosis-Noonan syndrome. Both the PTPN11 and NF1 (GENES, NF1) gene products are involved in the SIGNAL TRANSDUCTION pathway of Ras (RAS PROTEINS). 237.7 is a non-specific code that cannot be used to specify a diagnosis ICD-9-CM Diagnosis 237.70 Neurofibromatosis unspecified A group of disorders characterized by an autosomal dominant pattern of inheritance with high rates of spontaneous mutation and multiple neurofibromas or neurilemmomas. NEUROFIBROMATOSIS 1 (generalized neurofibromatosis) accounts for approximately 95% of cases, although multiple additional subtypes (e.g., NEUROFIBROMATOSIS 2, neurofibromatosis 3, etc.) have been described. (From Neurochirurgie 1998 Nov;44 237.70 is a specific code that can be used to specify a diagnosis 237.70 contains 3 index entries ICD-9-CM Diagnosis 237.71 Neurofibromatosis type 1 von recklinghausen's disease except of bone NF1. A rare genetic condition that causes brown spots and tumors on the skin, freckling in skin areas not exposed to the sun, tumors on the nerves, and developmental changes in the nervous system, muscles, bone, and skin. Type 1 (peripheral) neurofibromatosis (von Recklinghausen's disease), is the most common type of neurofibromatosis. It is characterized clinically by cutaneous and subcutaneous tumors with patches of hyperpigmentation. The hyperpigmented skin areas, are present from birth and found anywhere on the body surface. They can vary markedly in size and color. The dark brown areas are called cafe-au-lait spots. The multiple cutaneous and subcutaneous tumors are nerve sheath neoplasms, called neurofibromas. They can develop anywhere along the peripheral nerve fibers. Neurofibromas can become quite large, causing a major disfigurement, eroding bone, and compressing various peripheral nerve structures. Type 1 neurofibromatosis has dominant inheritance, with a gene locus on the proximal long arm of chromosome 17. -- 2003 An autosomal dominant inherited disorder (with a high frequency of spontaneous mutations) that features developmental changes in the nervous system, muscles, bones, and skin, most notably in tissue derived from the embryonic NEURAL CREST. Multiple hyperpigmented skin lesions and subcutaneous tumors are the hallmark of this disease. Peripheral and central nervous system neoplasms occur frequently, especially OPTIC NERVE GLIOMA and NEUROFIBROSARCOMA. NF1 is caused by mutations which inactivate the NF1 gene (GENES, NEUROFIBROMATOSIS 1) on chromosome 17q. The incidence of learning disabilities is also elevated in this condition. (From Adams et al., Principles of Neurology, 6th ed, pp1014-18) There is overlap of clinical features with NOONAN SYNDROME in a syndrome called neurofibromatosis-Noonan syndrome. Both the PTPN11 and NF1 (GENES, NF1) gene products are involved in the SIGNAL TRANSDUCTION pathway of Ras (RAS PROTEINS). 237.71 is a specific code that can be used to specify a diagnosis 237.71 contains 13 index entries ICD-9-CM Diagnosis 237.72 Neurofibromatosis type 2 acoustic neurofibromatosis An autosomal dominant disorder characterized by a high incidence of bilateral acoustic neuromas as well as schwannomas (NEURILEMMOMA) of other cranial and peripheral nerves, and other benign intracranial tumors including meningiomas, ependymomas, spinal neurofibromas, and gliomas. The disease has been linked to mutations of the NF2 gene (GENES, NEUROFIBROMATOSIS 2) on chromosome 22 (22q12) and usually presents clinically in the first or second decade of life. A genetic condition in which tumors form on the nerves of the inner ear and cause loss of hearing and balance. Tumors may also occur in the brain and on nerves in the skull and spinal cord, and may cause loss of speech, eye movement, and the ability to swallow. 237.72 is a specific code that can be used to specify a diagnosis 237.72 contains 4 index entries ICD-9-CM Diagnosis 237.9 Neoplasm of uncertain behavior of other and unspecified parts of nervous system 237.9 is a specific code that can be used to specify a diagnosis